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fatal insomnia

Prion disease of the human brain
Class type of: rare disease, inherited prion disease, genetic disease Q862872

Facts

15 properties
Instance of
class of disease, symptom or sign[2]
Subclass of
rare disease, inherited prion disease, genetic disease, thalamic disease, transmissible spongiform encephalopathy, insomnia[3][4][5][6][7][8]
Short name
FFI[23]
Age of onset
adult onset[28]
Genetic association
PRNP[27]
Has phenotype
dementia, Primary autonomic failure, depression, hallucination, anxiety, arterial hypertension, dysarthria, tachycardia, dysphagia, basal ganglia disease, Sleep-wake cycle disturbance, excessive tearing, sleep apnea, Short term memory impairment, Reduced attention regulation, diplopia, weight loss, fever, constipation, Loss of speech, adrenal gland hyperfunction[30][31][32][33][34][35][36][37][38][39][40][41][42][43]
Health specialty
psychiatry, sleep medicine, neuropathology[24][25][26]
ICD-9-CM
046.72[21]
ICPC 2 ID
N73[9]
NCI Thesaurus ID
C84711[22]
On focus list of Wikimedia project
WikiProject Medicine[29]
P14541
13u6Aj
P14914
D00466
Prevalence
+0.000001[20]
Symptoms and signs
agrypnia excitata, hallucination, arterial hypertension, fever, insomnia, panic attack, phobia, generalized anxiety disorder, ageing, dementia[10][11][12][13][14][15][16][17][18][19]
🏷️ Also known as
en fatal familial insomnia en Familial fatal insomnia en Insomnia, Fatal Familial en Insomnia familial fatal en FFI en Fatal insomnia ar أرق مميت ar أرق وراثي مميت cs Fatální familiární insomnie da Dødelig søvnløshed de Tödliche familiäre Schlaflosigkeit de Letale familiäre Insomnie de Familiäre fatale Insomnie el Θανάσιμη αϋπνία es Insomnio letal es insomnio familiar fatal es Insomnio familiar letal es Insomnio fatal fa بی‌خوابی خانوادگی مرگ‌آور fi fataali familiaalinen insomnia
🔖 Identifiers · 31
OpenAlex ID
C2779455247
Image (Wikimedia Commons)
Cranial imaging of a FFI patient.jpg ↗
Archive of Our Own tag
Fatal familial insomnia
BabelNet ID
03189477n
Bibliothèque nationale de France ID
13549188z
Disease Ontology ID
DOID:0050433
DiseasesDB
32177
Encyclopedia of China (Third Edition) ID
133490
Exact match
purl.obolibrary.org, identifiers.org, www.orpha.net
Freebase ID
/m/0b_bf
GARD rare disease ID
6429
GeneReviews ID
NBK1229
Show all 31 identifiers +19
ICD-10 ID
A81.981.9
ICD-10-CM
A81.83, A81.8
ICD-11 ID (Foundation)
669154658
ICD-11 ID (MMS)
8E02.2
ICD-9 ID
046.8046.8
KBpedia ID
FatalFamilialInsomnia
MeSH descriptor ID
D034062
MeSH tree code
C10.228.228.800.392, C10.574.843.512, C10.886.425.800.800.400, C01.207.800.392
Microsoft Academic ID (discontinued)
2779455247
Mondo ID
MONDO_0010808
OMIM ID
600072
Orphanet ID
466
Pschyrembel Online ID
tödliche familiäre Insomnie
Quora topic ID
Fatal-Familial-Insomnia
SNOMED CT ID
83157008
Subreddit
fatalfamilialinsomnia
UMLS CUI
C0206042
UniProt disease ID
DI-01607
WikiProjectMed ID
Fatal insomnia

Report an error or request removal Lineage (PROV-JSON)

🔗 Connections
Symptoms and signs 9
fever, arterial hypertension, dementia, insomnia, hallucination, phobia, ageing, panic attack +1 more
Subclass of 5
disease, insomnia, genetic disease, rare disease, transmissible spongiform encephalopathy
Health specialty 3
psychiatry, neuropathology, sleep medicine
Genetic association 1
PRNP
Instance of 1
symptom or sign
On focus list of Wikimedia project 1
WikiProject Medicine
← Genetic association 1
PRNP
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Summary

fatal insomnia is a class of disease[1].

Related Entities

disease psychiatry

References

Programmatic citations — every numbered marker resolves to a verifiable graph row below.

Direct Wikidata claims

  1. [2] ↑ . wikidata.org.
  2. [3] ↑ . Disease Ontology. Retrieved . wikidata.org.
  3. [4] ↑ . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  4. [5] ↑ . wikidata.org.
  5. [6] ↑ . wikidata.org.
  6. [7] ↑ . wikidata.org.
  7. [8] ↑ . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  8. [9] ↑ . wikidata.org.
  9. [10] ↑ . wikidata.org.
  10. [11] ↑ . Disease Ontology. Retrieved . wikidata.org.
  11. [12] ↑ . wikidata.org.
  12. [13] ↑ . wikidata.org.
  13. [14] ↑ . wikidata.org.
  14. [15] ↑ . wikidata.org.
  15. [16] ↑ . wikidata.org.
  16. [17] ↑ . wikidata.org.
  17. [18] ↑ . wikidata.org.
  18. [19] ↑ . wikidata.org.
  19. [20] ↑ . Retrieved . wikidata.org.
  20. [21] ↑ . Disease Ontology. Retrieved . wikidata.org.
  21. [22] ↑ . Disease Ontology. Retrieved . wikidata.org.
  22. [23] ↑ . wikidata.org.
  23. [24] ↑ . wikidata.org.
  24. [25] ↑ . wikidata.org.
  25. [26] ↑ . wikidata.org.
  26. [27] ↑ . UniProt. Retrieved . wikidata.org.
  27. [28] ↑ . Retrieved . wikidata.org.
  28. [29] ↑ . wikidata.org.
  29. [30] ↑ . Retrieved . wikidata.org.
  30. [31] ↑ . Retrieved . wikidata.org.
  31. [32] ↑ . Retrieved . wikidata.org.
  32. [33] ↑ . Retrieved . wikidata.org.
  33. [34] ↑ . Retrieved . wikidata.org.
  34. [35] ↑ . Retrieved . wikidata.org.
  35. [36] ↑ . Retrieved . wikidata.org.
  36. [37] ↑ . Retrieved . wikidata.org.
  37. [38] ↑ . Retrieved . wikidata.org.
  38. [39] ↑ . Retrieved . wikidata.org.
  39. [40] ↑ . Retrieved . wikidata.org.
  40. [41] ↑ . Retrieved . wikidata.org.
  41. [42] ↑ . Retrieved . wikidata.org.
  42. [43] ↑ . Retrieved . wikidata.org.

Class ancestry

  1. [1] ↑ . Wikidata. wikidata.org.

📑 Cite this page

Use these citations when quoting this entity in research, articles, AI prompts, or wherever provenance matters. We aggregate Wikidata + Wikipedia + authoritative open-data sources; the stitched, scored, cross-referenced view is what 4ort.xyz contributes.

APA 4ort.xyz Knowledge Graph. (2026). fatal insomnia. Retrieved November 3, 2026, from https://4ort.xyz/entity/fatal-insomnia
MLA “fatal insomnia.” 4ort.xyz Knowledge Graph, 4ort.xyz, 3 Nov. 2026, https://4ort.xyz/entity/fatal-insomnia.
BibTeX @misc{4ortxyz_fatal-insomnia_2026, author = {{4ort.xyz Knowledge Graph}}, title = {{fatal insomnia}}, year = {2026}, url = {https://4ort.xyz/entity/fatal-insomnia}, note = {Accessed: 2026-11-03}}
LLM prompt According to 4ort.xyz Knowledge Graph (aggregator of Wikidata, Wikipedia, and authoritative open-data sources): fatal insomnia — https://4ort.xyz/entity/fatal-insomnia (retrieved 2026-11-03)

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Edit History

Rolling log of changes to this entity's Wikidata record. Values shown reflect the current state of each edited property — follow the history link to see the precise diff for any edit.

  1. 12d ago · ACorrêa (WMB) · 2026-10-24 view diff on Wikidata ↗
    Sitelink count → 38
    Prevalence → {'amount': '+0.000001'}
    Wikipedia languages → ['ar', 'bg', 'bs', 'ca', 'commons', 'cs', 'da', 'de', 'el', 'en', 'es', 'et', 'e
    Age of onset → adult onset
    + 4 other properties edited (see Wikidata diff for full list)
    "/* wbeditentity-update:0| */ QuickStatements 3.0 [[:toollabs:qs-dev/batch/61469|batch #61469]]: Raras.org data import"
  2. 16w ago · Nyuhn · 2026-07-10 view diff on Wikidata ↗
    P14541 → 13u6Aj
    "/* wbeditentity-update:0| */ QuickStatements 3.0 [[:toollabs:qs-dev/batch/40849|batch #40849]]: ZGBK ID"
  3. 17w ago · JhealdBatch bot · 2026-07-03 view diff on Wikidata ↗
    Subclass of → rare disease, inherited prion disease, genetic disease +3
    "/* wbeditentity-update:0| */ QuickStatements 3.0 [[:toollabs:qs-dev/batch/39732|batch #39732]]: rm redundant subclass"
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