Gerstmann-Straussler-Scheinker syndrome

prion disease characterized by adult onset of memory loss, dementia, ataxia, and pathologic deposition of amyloid-like plaques in the brain
MedicalCondition rare_disease Q383228
Gerstmann-Straussler-Scheinker syndrome
Press Enter · cited answer in seconds

Gerstmann-Straussler-Scheinker syndrome

Summary

Gerstmann-Straussler-Scheinker syndrome is a rare disease[1]. It ranks in the top 8% of rare_disease entities by monthly Wikipedia readership (1,019 views/month).[2]

Key Facts

  • Gerstmann-Straussler-Scheinker syndrome's instance of is recorded as rare disease[3].
  • Gerstmann-Straussler-Scheinker syndrome's instance of is recorded as class of disease[4].
  • Gerstmann-Straussler-Scheinker syndrome's instance of is recorded as symptom or sign[5].
  • Josef Gerstmann is named after Gerstmann-Straussler-Scheinker syndrome[6].
  • Ernst Sträussler is named after Gerstmann-Straussler-Scheinker syndrome[7].
  • Ilya Scheinker is named after Gerstmann-Straussler-Scheinker syndrome[8].
  • Gerstmann-Straussler-Scheinker syndrome is a type of transmissible spongiform encephalopathy[9].
  • Gerstmann-Straussler-Scheinker syndrome is a type of inherited prion disease[10].
  • Gerstmann-Straussler-Scheinker syndrome is a type of disease[11].
  • Gerstmann-Straussler-Scheinker syndrome's Commons category is recorded as Gerstmann–Sträussler–Scheinker syndrome[12].
  • Gerstmann-Straussler-Scheinker syndrome's ICPC 2 ID is recorded as N73[13].
  • Gerstmann-Straussler-Scheinker syndrome's symptoms and signs is recorded as ataxia[14].
  • Gerstmann-Straussler-Scheinker syndrome's symptoms and signs is recorded as dementia[15].
  • Gerstmann-Straussler-Scheinker syndrome's medical examination is recorded as magnetic resonance imaging[16].
  • Gerstmann-Straussler-Scheinker syndrome's medical examination is recorded as biopsy[17].
  • Gerstmann-Straussler-Scheinker syndrome's medical examination is recorded as medical history[18].
  • Gerstmann-Straussler-Scheinker syndrome's medical examination is recorded as histopathology[19].
  • Gerstmann-Straussler-Scheinker syndrome's possible treatment is recorded as symptomatic treatment[20].
  • Gerstmann-Straussler-Scheinker syndrome's ICD-9-CM is recorded as 046.71[21].
  • Gerstmann-Straussler-Scheinker syndrome's NCI Thesaurus ID is recorded as C84727[22].
  • Gerstmann-Straussler-Scheinker syndrome's health specialty is recorded as neurology[23].
  • Gerstmann-Straussler-Scheinker syndrome's genetic association is recorded as PRNP[24].
  • Gerstmann-Straussler-Scheinker syndrome's exact match is recorded as http://purl.obolibrary.org/obo/DOID_4249[25].
  • Gerstmann-Straussler-Scheinker syndrome's exact match is recorded as http://identifiers.org/doid/DOID:4249[26].
  • Gerstmann-Straussler-Scheinker syndrome's exact match is recorded as http://www.orpha.net/ORDO/Orphanet_356[27].

Why It Matters

Gerstmann-Straussler-Scheinker syndrome ranks in the top 8% of rare_disease entities by monthly Wikipedia readership (1,019 views/month).[2] It has Wikipedia articles in 19 language editions, a strong signal of global cultural recognition.[28] It is known by 15 alternative names across languages and contexts.[29]

References

Programmatic citations — every numbered marker resolves to a verifiable graph row below.

Direct Wikidata claims

  1. [3] . wikidata.org.
  2. [4] . wikidata.org.
  3. [5] . wikidata.org.
  4. [6] . wikidata.org.
  5. [7] . wikidata.org.
  6. [8] . wikidata.org.
  7. [9] . Disease Ontology. Retrieved . wikidata.org.
  8. [10] . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  9. [11] . wikidata.org.
  10. [12] . wikidata.org.
  11. [13] . wikidata.org.
  12. [14] . wikidata.org.
  13. [15] . wikidata.org.
  14. [16] . wikidata.org.
  15. [17] . wikidata.org.
  16. [18] . wikidata.org.
  17. [19] . wikidata.org.
  18. [20] . wikidata.org.
  19. [21] . Disease Ontology. Retrieved . wikidata.org.
  20. [22] . Disease Ontology. Retrieved . wikidata.org.
  21. [23] . wikidata.org.
  22. [24] . Q905695. Retrieved . platform.opentargets.org. Provenance: wikidata.org.
  23. [25] . Disease Ontology. Retrieved . wikidata.org.
  24. [26] . Identifiers.org. registry.identifiers.org. Provenance: wikidata.org.
  25. [27] . wikidata.org.

Class ancestry

  1. [1] . Wikidata. wikidata.org.

Aggregate / graph-position facts

  1. [2] . Wikimedia Foundation. dumps.wikimedia.org.
  2. [28] . Wikidata sitelinks. wikidata.org.
  3. [29] . Wikidata aliases. wikidata.org.

📑 Cite this page

Use these citations when quoting this entity in research, articles, AI prompts, or wherever provenance matters. We aggregate Wikidata + Wikipedia + authoritative open-data sources; the stitched, scored, cross-referenced view is what 4ort.xyz contributes.

APA 4ort.xyz Knowledge Graph. (2026). Gerstmann-Straussler-Scheinker syndrome. Retrieved May 3, 2026, from https://4ort.xyz/entity/gerstmann-straussler-scheinker-syndrome
MLA “Gerstmann-Straussler-Scheinker syndrome.” 4ort.xyz Knowledge Graph, 4ort.xyz, 3 May. 2026, https://4ort.xyz/entity/gerstmann-straussler-scheinker-syndrome.
BibTeX @misc{4ortxyz_gerstmann-straussler-scheinker-syndrome_2026, author = {{4ort.xyz Knowledge Graph}}, title = {{Gerstmann-Straussler-Scheinker syndrome}}, year = {2026}, url = {https://4ort.xyz/entity/gerstmann-straussler-scheinker-syndrome}, note = {Accessed: 2026-05-03}}
LLM prompt According to 4ort.xyz Knowledge Graph (aggregator of Wikidata, Wikipedia, and authoritative open-data sources): Gerstmann-Straussler-Scheinker syndrome — https://4ort.xyz/entity/gerstmann-straussler-scheinker-syndrome (retrieved 2026-05-03)

Canonical URL: https://4ort.xyz/entity/gerstmann-straussler-scheinker-syndrome · Last refreshed:

Edit History

Rolling log of changes to this entity's Wikidata record. Values shown reflect the current state of each edited property — follow the history link to see the precise diff for any edit.

  1. 27d ago · ~2026-28752-62 · 2026-05-12 view diff on Wikidata ↗
    Aliases
    Possible treatment symptomatic treatment
    Genetic association PRNP
    Medical examination magnetic resonance imaging, biopsy, medical history +1
    + 9 other properties edited (see Wikidata diff for full list)
    "/* wbsetclaim-create:2||1 */ [[Property:P780]]: [[Q767669]]"
Live feed via Wikidata EventStreams. New edits appear within minutes of being made on Wikidata.