tyrosinemia type III

tyrosinemia that has material basis in deficiency of 4-hydroxyphenylpyruvate dioxygenase disrupting the break down of tyrosine
MedicalCondition designated_intractable_rare_disease Q7861692
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tyrosinemia type III

Summary

tyrosinemia type III is a designated intractable/rare disease[1]. It draws 3 Wikipedia views per month (designated_intractable_rare_disease category, ranking #167 of 201).[2]

Key Facts

  • tyrosinemia type III's instance of is recorded as designated intractable/rare disease[3].
  • tyrosinemia type III's instance of is recorded as rare disease[4].
  • tyrosinemia type III's instance of is recorded as class of disease[5].
  • tyrosinemia type III's subclass of is recorded as tyrosinemia[6].
  • tyrosinemia type III's OMIM ID is recorded as 276710[7].
  • tyrosinemia type III's ICD-9 ID is recorded as 270.2[8].
  • tyrosinemia type III's ICD-10 ID is recorded as E70.2[9].
  • tyrosinemia type III's DiseasesDB is recorded as 29836[10].
  • tyrosinemia type III's Disease Ontology ID is recorded as DOID:0050727[11].
  • tyrosinemia type III's external data available at URL is recorded as http://www.nanbyou.or.jp/entry/4696[12].
  • tyrosinemia type III's Orphanet ID is recorded as 69723[13].
  • tyrosinemia type III's health specialty is recorded as endocrinology[14].
  • tyrosinemia type III's drug or therapy used for treatment is recorded as nitisinone[15].
  • tyrosinemia type III's drug or therapy used for treatment is recorded as sodium ascorbate[16].
  • tyrosinemia type III's genetic association is recorded as HPD[17].
  • tyrosinemia type III's exact match is recorded as http://purl.obolibrary.org/obo/DOID_0050727[18].
  • tyrosinemia type III's exact match is recorded as http://identifiers.org/doid/DOID:0050727[19].
  • tyrosinemia type III's PatientsLikeMe condition ID is recorded as tyrosinemia-type-iii[20].
  • tyrosinemia type III's GARD rare disease ID is recorded as 10332[21].
  • tyrosinemia type III's on focus list of Wikimedia project is recorded as WikiProject Medicine[22].
  • tyrosinemia type III's Mondo ID is recorded as MONDO_0010162[23].
  • tyrosinemia type III's Microsoft Academic ID is recorded as 2775904740[24].
  • tyrosinemia type III's has phenotype is recorded as Hypertyrosinemia[25].
  • tyrosinemia type III's UniProt disease ID is recorded as DI-01109[26].

Why It Matters

tyrosinemia type III draws 3 Wikipedia views per month (designated_intractable_rare_disease category, ranking #167 of 201).[2]

References

Programmatic citations — every numbered marker resolves to a verifiable graph row below.

Direct Wikidata claims

  1. [3] . ddrare.nibiohn.go.jp. Retrieved . ddrare.nibiohn.go.jp. Provenance: wikidata.org.
  2. [4] . wikidata.org.
  3. [5] . wikidata.org.
  4. [6] . Disease Ontology. Retrieved . wikidata.org.
  5. [7] . Disease Ontology. Retrieved . wikidata.org.
  6. [8] . wikidata.org.
  7. [9] . wikidata.org.
  8. [10] . wikidata.org.
  9. [11] . Disease Ontology. Retrieved . wikidata.org.
  10. [12] . ddrare.nibiohn.go.jp. Retrieved . ddrare.nibiohn.go.jp. Provenance: wikidata.org.
  11. [13] . wikidata.org.
  12. [14] . wikidata.org.
  13. [15] . NDF-RT. Retrieved . wikidata.org.
  14. [16] . NDF-RT. Retrieved . wikidata.org.
  15. [17] . Mutations in the 4-hydroxyphenylpyruvate dioxygenase gene (HPD) in patients with tyrosinemia type III. Retrieved . platform.opentargets.org. Provenance: wikidata.org.
  16. [18] . Disease Ontology. Retrieved . wikidata.org.
  17. [19] . Identifiers.org. registry.identifiers.org. Provenance: wikidata.org.
  18. [20] . wikidata.org.
  19. [21] . wikidata.org.
  20. [22] . wikidata.org.
  21. [23] . wikidata.org.
  22. [24] . wikidata.org.
  23. [25] . Disease Ontology. Retrieved . wikidata.org.
  24. [26] . wikidata.org.

Class ancestry

  1. [1] . Wikidata. wikidata.org.

Aggregate / graph-position facts

  1. [2] . Wikimedia Foundation. dumps.wikimedia.org.

📑 Cite this page

Use these citations when quoting this entity in research, articles, AI prompts, or wherever provenance matters. We aggregate Wikidata + Wikipedia + authoritative open-data sources; the stitched, scored, cross-referenced view is what 4ort.xyz contributes.

APA 4ort.xyz Knowledge Graph. (2026). tyrosinemia type III. Retrieved May 3, 2026, from https://4ort.xyz/entity/tyrosinemia-type-iii
MLA “tyrosinemia type III.” 4ort.xyz Knowledge Graph, 4ort.xyz, 3 May. 2026, https://4ort.xyz/entity/tyrosinemia-type-iii.
BibTeX @misc{4ortxyz_tyrosinemia-type-iii_2026, author = {{4ort.xyz Knowledge Graph}}, title = {{tyrosinemia type III}}, year = {2026}, url = {https://4ort.xyz/entity/tyrosinemia-type-iii}, note = {Accessed: 2026-05-03}}
LLM prompt According to 4ort.xyz Knowledge Graph (aggregator of Wikidata, Wikipedia, and authoritative open-data sources): tyrosinemia type III — https://4ort.xyz/entity/tyrosinemia-type-iii (retrieved 2026-05-03)

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