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primary sclerosing cholangitis

sclerosing cholangitis characterized by fibroobliterative inflammation of the biliary tract, leading to cirrhosis and portal hypertension
Class type of: liver disease, sclerosing cholangitis, genetic biliary tract disease Q1058608

Facts

13 properties
Instance of
designated intractable/rare disease, class of disease, symptom or sign[2][3]
Subclass of
liver disease, sclerosing cholangitis, genetic biliary tract disease[4][5][6]
Age of onset
juvenile onset, adult onset, childhood onset, late onset[16][17][18][19]
Genetic association
GPR35, MST1, SEMA4D, TCF4[12][13][14][15]
Has effect
liver cirrhosis[9]
Has phenotype
Abnormal biliary tract morphology, liver fibrosis, portal hypertension, splenomegaly, fever, depression, osteopenia, gallstone disease, abdominal pain, hypoalbuminemia, vitamin A deficiency, hepatitis, vitamin D deficiency, vitamin E deficiency, end-stage liver disease, thyroiditis, encephalopathy, gallbladder cancer[21][22][23][24][25][26][27][28][29][30][31][32][33][34]
Health specialty
gastroenterology[11]
ICPC 2 ID
D98[7]
NCI Thesaurus ID
C4828[10]
On focus list of Wikimedia project
WikiProject Medicine[20]
P14541
2M0BvJ[35]
P14914
D00171[36]
Prevalence
+0.00005[8]
🏷️ Also known as
en primary sclerosing cholangitis en CHOLANGITIS, PRIMARY SCLEROSING en CHOLANGITIS, PRIMARY SCLEROSING; PSC en PSC; primary sclerosing cholangitis en PSC en Primary sclerosing cholangitis ar التهاب الأقنية الصفراوية المصلب الابتدائي ar Primary sclerosing cholangitis ar التهاب الأوعية الصفراوية المصلب الابتدائي cs primární sklerozující cholangitis cs primární sklerozující cholangitida da Primær skleroserende kolangitis de Primär sklerosierende Cholangitis es Colangitis esclerosante es colangitis esclerosante primaria fi Primaarinen sklerosoiva kolangiitti fi Primaari sklerosoiva kolangiitti fi Sklerosoiva kolangiitti fr Cholangite primaire sclérosante fr Cholangite sclerosante primitive
🔖 Identifiers · 29
OpenAlex ID
C2780615123
Image (Wikimedia Commons)
Cholangiogram of primary sclerosing cholangitis.jpg ↗
BabelNet ID
03750313n
Disease Ontology ID
DOID:0060643
DiseasesDB
10643
EMedicine ID
187724
Encyclopedia of China (Third Edition) ID
579723
Exact match
purl.obolibrary.org, identifiers.org, www.orpha.net
External data available at URL
www.nanbyou.or.jp
Freebase ID
/m/03jlrw
GARD rare disease ID
1280
Genetics Home Reference Conditions ID
primary-sclerosing-cholangitis
Show all 29 identifiers +17
ICD-10-CM
K83.0
ICD-11 ID (Foundation)
857962451
ICD-11 ID (MMS)
DB96.2
ICD-9 ID
576.1
JSTOR topic ID (archived)
sclerosing-cholangitis
KEGG ID
H01684
MeSH descriptor ID
C536419
MedlinePlus ID
000285
Mondo ID
MONDO_0013433
OMIM ID
613806
Orphanet ID
171
Patientplus ID
primary-sclerosing-cholangitis-pro
PatientsLikeMe condition ID
primary-sclerosing-cholangitis-sclerosing-cholangitis
UK Parliament thesaurus ID
554551
UMLS CUI
C0566602
WikiProjectMed ID
Primary sclerosing cholangitis
WikiSkripta article ID
42934

Report an error or request removal Lineage (PROV-JSON)

🔗 Connections
Subclass of 2
disease, liver disease
Has effect 1
liver cirrhosis
Health specialty 1
gastroenterology
Instance of 1
symptom or sign
On focus list of Wikimedia project 1
WikiProject Medicine
← Has cause 1
liver cirrhosis
← Medical condition 1
Elena Baltacha
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Summary

primary sclerosing cholangitis is a designated intractable/rare disease[1].

Related Entities

disease Elena Baltacha

References

Programmatic citations — every numbered marker resolves to a verifiable graph row below.

Direct Wikidata claims

  1. [2] ↑ . wikidata.org.
  2. [3] ↑ . wikidata.org.
  3. [4] ↑ . Pharmacological interventions for primary sclerosing cholangitis: an attempted network meta-analysis.. wikidata.org.
  4. [5] ↑ . British Society of Gastroenterology and UK-PSC guidelines for the diagnosis and management of primary sclerosing cholangitis. Retrieved . wikidata.org.
  5. [6] ↑ . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  6. [7] ↑ . wikidata.org.
  7. [8] ↑ . Retrieved . wikidata.org.
  8. [9] ↑ . wikidata.org.
  9. [10] ↑ . Disease Ontology. Retrieved . wikidata.org.
  10. [11] ↑ . wikidata.org.
  11. [12] ↑ . Retrieved . wikidata.org.
  12. [13] ↑ . Retrieved . wikidata.org.
  13. [14] ↑ . Retrieved . wikidata.org.
  14. [15] ↑ . Retrieved . wikidata.org.
  15. [16] ↑ . Retrieved . wikidata.org.
  16. [17] ↑ . Retrieved . wikidata.org.
  17. [18] ↑ . Retrieved . wikidata.org.
  18. [19] ↑ . Retrieved . wikidata.org.
  19. [20] ↑ . wikidata.org.
  20. [21] ↑ . Retrieved . wikidata.org.
  21. [22] ↑ . Retrieved . wikidata.org.
  22. [23] ↑ . Retrieved . wikidata.org.
  23. [24] ↑ . Retrieved . wikidata.org.
  24. [25] ↑ . Retrieved . wikidata.org.
  25. [26] ↑ . Retrieved . wikidata.org.
  26. [27] ↑ . Retrieved . wikidata.org.
  27. [28] ↑ . Retrieved . wikidata.org.
  28. [29] ↑ . Retrieved . wikidata.org.
  29. [30] ↑ . Retrieved . wikidata.org.
  30. [31] ↑ . Retrieved . wikidata.org.
  31. [32] ↑ . Retrieved . wikidata.org.
  32. [33] ↑ . Retrieved . wikidata.org.
  33. [34] ↑ . Retrieved . wikidata.org.
  34. [35] ↑ . wikidata.org.
  35. [36] ↑ . wikidata.org.

Class ancestry

  1. [1] ↑ . Wikidata. wikidata.org.

📑 Cite this page

Use these citations when quoting this entity in research, articles, AI prompts, or wherever provenance matters. We aggregate Wikidata + Wikipedia + authoritative open-data sources; the stitched, scored, cross-referenced view is what 4ort.xyz contributes.

APA 4ort.xyz Knowledge Graph. (2026). primary sclerosing cholangitis. Retrieved November 6, 2026, from https://4ort.xyz/entity/primary-sclerosing-cholangitis
MLA “primary sclerosing cholangitis.” 4ort.xyz Knowledge Graph, 4ort.xyz, 6 Nov. 2026, https://4ort.xyz/entity/primary-sclerosing-cholangitis.
BibTeX @misc{4ortxyz_primary-sclerosing-cholangitis_2026, author = {{4ort.xyz Knowledge Graph}}, title = {{primary sclerosing cholangitis}}, year = {2026}, url = {https://4ort.xyz/entity/primary-sclerosing-cholangitis}, note = {Accessed: 2026-11-06}}
LLM prompt According to 4ort.xyz Knowledge Graph (aggregator of Wikidata, Wikipedia, and authoritative open-data sources): primary sclerosing cholangitis — https://4ort.xyz/entity/primary-sclerosing-cholangitis (retrieved 2026-11-06)

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Edit History

Rolling log of changes to this entity's Wikidata record. Values shown reflect the current state of each edited property — follow the history link to see the precise diff for any edit.

  1. 15d ago · ACorrêa (WMB) · 2026-10-23 view diff on Wikidata ↗
    Genetic association → GPR35, MST1, SEMA4D +1
    Prevalence → {'amount': '+0.00005'}
    Wikipedia languages → ['ar', 'az', 'bs', 'ca', 'commons', 'da', 'de', 'en', 'es', 'et', 'fi', 'fr', 'h
    Age of onset → juvenile onset, adult onset, childhood onset +1
    + 3 other properties edited (see Wikidata diff for full list)
    "/* wbeditentity-update:0| */ QuickStatements 3.0 [[:toollabs:qs-dev/batch/61469|batch #61469]]: Raras.org data import"
  2. 17w ago · Nyuhn · 2026-07-10 view diff on Wikidata ↗
    P14541 → 2M0BvJ
    "/* wbeditentity-update:0| */ QuickStatements 3.0 [[:toollabs:qs-dev/batch/40849|batch #40849]]: ZGBK ID"
  3. 18w ago · JhealdBatch bot · 2026-07-03 view diff on Wikidata ↗
    Health specialty → gastroenterology
    Subclass of → —
    Instance of → designated intractable/rare disease, class of disease, symptom or sign
    Instance of → —
    + 4 other properties edited (see Wikidata diff for full list)
    "/* wbeditentity-update:0| */ QuickStatements 3.0 [[:toollabs:qs-dev/batch/39732|batch #39732]]: rm redundant subclass"
Live feed via Wikidata EventStreams. New edits appear within minutes of being made on Wikidata.