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primary pulmonary hypertension

chronic pulmonary heart disease characterized by an increase of blood pressure in the pulmonary artery, pulmonary vein, or pulmonary capillaries, among others, has symptoms shortness of breath, dizziness, fainting, leg swelling
MedicalCondition rare_disease Q18554794
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primary pulmonary hypertension

Summary

primary pulmonary hypertension is a rare disease[1].

Key Facts

  • primary pulmonary hypertension's instance of is recorded as rare disease[2].
  • primary pulmonary hypertension's instance of is recorded as class of disease[3].
  • primary pulmonary hypertension's subclass of is recorded as chronic pulmonary heart disease[4].
  • primary pulmonary hypertension's subclass of is recorded as pulmonary hypertension[5].
  • primary pulmonary hypertension's MeSH descriptor ID is recorded as D065627[6].
  • primary pulmonary hypertension's OMIM ID is recorded as 615342[7].
  • primary pulmonary hypertension's OMIM ID is recorded as 178600[8].
  • primary pulmonary hypertension's OMIM ID is recorded as 615343[9].
  • primary pulmonary hypertension's OMIM ID is recorded as 615344[10].
  • primary pulmonary hypertension's OMIM ID is recorded as 265400[11].
  • primary pulmonary hypertension's KEGG ID is recorded as H01619[12].
  • primary pulmonary hypertension's MeSH tree code is recorded as C08.381.423.300[13].
  • primary pulmonary hypertension's Disease Ontology ID is recorded as DOID:14557[14].
  • primary pulmonary hypertension's Orphanet ID is recorded as 422[15].
  • primary pulmonary hypertension's ICD-9-CM is recorded as 416.0[16].
  • primary pulmonary hypertension's NCI Thesaurus ID is recorded as C97119[17].
  • primary pulmonary hypertension's health specialty is recorded as cardiology[18].
  • primary pulmonary hypertension's drug or therapy used for treatment is recorded as prostacyclin[19].
  • primary pulmonary hypertension's genetic association is recorded as BMPR2[20].
  • primary pulmonary hypertension's genetic association is recorded as SMAD9[21].
  • primary pulmonary hypertension's genetic association is recorded as KCNK3[22].
  • primary pulmonary hypertension's genetic association is recorded as CAV1[23].
  • primary pulmonary hypertension's exact match is recorded as http://purl.obolibrary.org/obo/DOID_14557[24].
  • primary pulmonary hypertension's exact match is recorded as http://identifiers.org/doid/DOID:14557[25].
  • primary pulmonary hypertension's exact match is recorded as http://www.orpha.net/ORDO/Orphanet_422[26].

References

Programmatic citations — every numbered marker resolves to a verifiable graph row below.

Direct Wikidata claims

  1. [2] ↑ . wikidata.org.
  2. [3] ↑ . wikidata.org.
  3. [4] ↑ . Disease Ontology. Retrieved . wikidata.org.
  4. [5] ↑ . wikidata.org.
  5. [6] ↑ . wikidata.org.
  6. [7] ↑ . Disease Ontology. Retrieved . wikidata.org.
  7. [8] ↑ . Disease Ontology. Retrieved . wikidata.org.
  8. [9] ↑ . Disease Ontology. Retrieved . wikidata.org.
  9. [10] ↑ . Disease Ontology. Retrieved . wikidata.org.
  10. [11] ↑ . Disease Ontology. Retrieved . wikidata.org.
  11. [12] ↑ . wikidata.org.
  12. [13] ↑ . wikidata.org.
  13. [14] ↑ . Disease Ontology. Retrieved . wikidata.org.
  14. [15] ↑ . Disease Ontology. Retrieved . wikidata.org.
  15. [16] ↑ . Disease Ontology. Retrieved . wikidata.org.
  16. [17] ↑ . Disease Ontology. Retrieved . wikidata.org.
  17. [18] ↑ . wikidata.org.
  18. [19] ↑ . Inxight: Drugs Database. Retrieved . drugs.ncats.io. Provenance: wikidata.org.
  19. [20] ↑ . Heterozygous germline mutations in BMPR2, encoding a TGF-beta receptor, cause familial primary pulmonary hypertension. wikidata.org.
  20. [21] ↑ . A new nonsense mutation of SMAD8 associated with pulmonary arterial hypertension. wikidata.org.
  21. [22] ↑ . A novel channelopathy in pulmonary arterial hypertension. wikidata.org.
  22. [23] ↑ . Whole exome sequencing to identify a novel gene (caveolin-1) associated with human pulmonary arterial hypertension. wikidata.org.
  23. [24] ↑ . Disease Ontology. Retrieved . wikidata.org.
  24. [25] ↑ . Identifiers.org. registry.identifiers.org. Provenance: wikidata.org.
  25. [26] ↑ . wikidata.org.

Class ancestry

  1. [1] ↑ . Wikidata. wikidata.org.

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Use these citations when quoting this entity in research, articles, AI prompts, or wherever provenance matters. We aggregate Wikidata + Wikipedia + authoritative open-data sources; the stitched, scored, cross-referenced view is what 4ort.xyz contributes.

APA 4ort.xyz Knowledge Graph. (2026). primary pulmonary hypertension. Retrieved May 3, 2026, from https://4ort.xyz/entity/primary-pulmonary-hypertension
MLA “primary pulmonary hypertension.” 4ort.xyz Knowledge Graph, 4ort.xyz, 3 May. 2026, https://4ort.xyz/entity/primary-pulmonary-hypertension.
BibTeX @misc{4ortxyz_primary-pulmonary-hypertension_2026, author = {{4ort.xyz Knowledge Graph}}, title = {{primary pulmonary hypertension}}, year = {2026}, url = {https://4ort.xyz/entity/primary-pulmonary-hypertension}, note = {Accessed: 2026-05-03}}
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