primary cutaneous amyloidosis

amyloidosis characterized by pruritus, skin scratching and by deposits of amyloid in the dermis
MedicalCondition rare_disease Q7243115
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primary cutaneous amyloidosis

Summary

primary cutaneous amyloidosis is a rare disease[1]. It draws 11 Wikipedia views per month (rare_disease category, ranking #231 of 627).[2]

Key Facts

  • primary cutaneous amyloidosis's instance of is recorded as rare disease[3].
  • primary cutaneous amyloidosis's instance of is recorded as class of disease[4].
  • primary cutaneous amyloidosis's subclass of is recorded as amyloidosis[5].
  • primary cutaneous amyloidosis's subclass of is recorded as skin disease[6].
  • primary cutaneous amyloidosis's Commons category is recorded as Primary cutaneous amyloidosis[7].
  • primary cutaneous amyloidosis's MeSH descriptor ID is recorded as C562643[8].
  • primary cutaneous amyloidosis's OMIM ID is recorded as 613955[9].
  • primary cutaneous amyloidosis's OMIM ID is recorded as 105250[10].
  • primary cutaneous amyloidosis's ICD-9 ID is recorded as 277.3[11].
  • primary cutaneous amyloidosis's DiseasesDB is recorded as 29871[12].
  • primary cutaneous amyloidosis's KEGG ID is recorded as H01217[13].
  • primary cutaneous amyloidosis's Disease Ontology ID is recorded as DOID:0050639[14].
  • primary cutaneous amyloidosis's anatomical location is recorded as zone of skin[15].
  • primary cutaneous amyloidosis's Orphanet ID is recorded as 353220[16].
  • primary cutaneous amyloidosis's Orphanet ID is recorded as 137807[17].
  • primary cutaneous amyloidosis's health specialty is recorded as dermatology[18].
  • primary cutaneous amyloidosis's genetic association is recorded as IL31RA[19].
  • primary cutaneous amyloidosis's genetic association is recorded as OSMR[20].
  • primary cutaneous amyloidosis's exact match is recorded as http://purl.obolibrary.org/obo/DOID_0050639[21].
  • primary cutaneous amyloidosis's exact match is recorded as http://identifiers.org/doid/DOID:0050639[22].
  • primary cutaneous amyloidosis's exact match is recorded as http://www.orpha.net/ORDO/Orphanet_137807[23].
  • primary cutaneous amyloidosis's exact match is recorded as http://www.orpha.net/ORDO/Orphanet_353220[24].
  • primary cutaneous amyloidosis's UMLS CUI is recorded as C0268397[25].
  • primary cutaneous amyloidosis's ICD-10-CM is recorded as L99.0*[26].
  • primary cutaneous amyloidosis's ICD-10-CM is recorded as E85.4+[27].

Why It Matters

primary cutaneous amyloidosis draws 11 Wikipedia views per month (rare_disease category, ranking #231 of 627).[2]

References

Programmatic citations — every numbered marker resolves to a verifiable graph row below.

Direct Wikidata claims

  1. [3] ↑ . wikidata.org.
  2. [4] ↑ . wikidata.org.
  3. [5] ↑ . Disease Ontology. Retrieved . wikidata.org.
  4. [6] ↑ . Disease Ontology. Retrieved . wikidata.org.
  5. [7] ↑ . wikidata.org.
  6. [8] ↑ . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  7. [9] ↑ . Disease Ontology. Retrieved . wikidata.org.
  8. [10] ↑ . Disease Ontology. Retrieved . wikidata.org.
  9. [11] ↑ . wikidata.org.
  10. [12] ↑ . wikidata.org.
  11. [13] ↑ . wikidata.org.
  12. [14] ↑ . Disease Ontology. Retrieved . wikidata.org.
  13. [15] ↑ . Disease Ontology. Retrieved . wikidata.org.
  14. [16] ↑ . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  15. [17] ↑ . Disease Ontology. Retrieved . wikidata.org.
  16. [18] ↑ . wikidata.org.
  17. [19] ↑ . Novel IL31RA gene mutation and ancestral OSMR mutant allele in familial primary cutaneous amyloidosis. wikidata.org.
  18. [20] ↑ . Oncostatin M receptor-beta mutations underlie familial primary localized cutaneous amyloidosis. wikidata.org.
  19. [21] ↑ . Disease Ontology. Retrieved . wikidata.org.
  20. [22] ↑ . Identifiers.org. ebi.ac.uk. Provenance: wikidata.org.
  21. [23] ↑ . wikidata.org.
  22. [24] ↑ . wikidata.org.
  23. [25] ↑ . UMLS 2023. Retrieved . wikidata.org.
  24. [26] ↑ . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  25. [27] ↑ . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.

Class ancestry

  1. [1] ↑ . Wikidata. wikidata.org.

Aggregate / graph-position facts

  1. [2] ↑ . Wikimedia Foundation. dumps.wikimedia.org.

📑 Cite this page

Use these citations when quoting this entity in research, articles, AI prompts, or wherever provenance matters. We aggregate Wikidata + Wikipedia + authoritative open-data sources; the stitched, scored, cross-referenced view is what 4ort.xyz contributes.

APA 4ort.xyz Knowledge Graph. (2026). primary cutaneous amyloidosis. Retrieved October 4, 2026, from https://4ort.xyz/entity/primary-cutaneous-amyloidosis
MLA “primary cutaneous amyloidosis.” 4ort.xyz Knowledge Graph, 4ort.xyz, 4 Oct. 2026, https://4ort.xyz/entity/primary-cutaneous-amyloidosis.
BibTeX @misc{4ortxyz_primary-cutaneous-amyloidosis_2026, author = {{4ort.xyz Knowledge Graph}}, title = {{primary cutaneous amyloidosis}}, year = {2026}, url = {https://4ort.xyz/entity/primary-cutaneous-amyloidosis}, note = {Accessed: 2026-10-04}}
LLM prompt According to 4ort.xyz Knowledge Graph (aggregator of Wikidata, Wikipedia, and authoritative open-data sources): primary cutaneous amyloidosis — https://4ort.xyz/entity/primary-cutaneous-amyloidosis (retrieved 2026-10-04)

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