Leber congenital amaurosis 2

Leber congenital amaurosis that is characterized by night blindness, some transient improvement in vision, and eventual progressive visual loss and has material basis in mutation in the RPE65 gene on chromosome 1
MedicalCondition rare_disease Q27677590
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Leber congenital amaurosis 2

Summary

Leber congenital amaurosis 2 is a rare disease[1].

Key Facts

  • Leber congenital amaurosis 2's instance of is recorded as rare disease[2].
  • Leber congenital amaurosis 2's instance of is recorded as class of disease[3].
  • Leber congenital amaurosis 2's subclass of is recorded as Leber congenital amaurosis[4].
  • Leber congenital amaurosis 2's subclass of is recorded as genetic disease[5].
  • Leber congenital amaurosis 2's MeSH descriptor ID is recorded as C536601[6].
  • Leber congenital amaurosis 2's OMIM ID is recorded as 204100[7].
  • Leber congenital amaurosis 2's Disease Ontology ID is recorded as DOID:0110016[8].
  • Leber congenital amaurosis 2's genetic association is recorded as RPE65[9].
  • Leber congenital amaurosis 2's exact match is recorded as http://purl.obolibrary.org/obo/DOID_0110016[10].
  • Leber congenital amaurosis 2's exact match is recorded as http://identifiers.org/doid/DOID:0110016[11].
  • Leber congenital amaurosis 2's UMLS CUI is recorded as C1859844[12].
  • Leber congenital amaurosis 2's ICD-10-CM is recorded as H35.5[13].
  • Leber congenital amaurosis 2's GARD rare disease ID is recorded as 636[14].
  • Leber congenital amaurosis 2's on focus list of Wikimedia project is recorded as WikiProject Medicine[15].
  • Leber congenital amaurosis 2's Mondo ID is recorded as MONDO_0008765[16].
  • Leber congenital amaurosis 2's UniProt disease ID is recorded as DI-00630[17].

References

Programmatic citations — every numbered marker resolves to a verifiable graph row below.

Direct Wikidata claims

  1. [2] . wikidata.org.
  2. [3] . wikidata.org.
  3. [4] . Disease Ontology. Retrieved . wikidata.org.
  4. [5] . Disease Ontology. Retrieved . wikidata.org.
  5. [6] . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  6. [7] . Disease Ontology. Retrieved . wikidata.org.
  7. [8] . Disease Ontology. Retrieved . wikidata.org.
  8. [9] . Q905695. Retrieved . wikidata.org.
  9. [10] . Disease Ontology. Retrieved . wikidata.org.
  10. [11] . Identifiers.org. ebi.ac.uk. Provenance: wikidata.org.
  11. [12] . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  12. [13] . Disease Ontology. Retrieved . wikidata.org.
  13. [14] . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  14. [15] . wikidata.org.
  15. [16] . wikidata.org.
  16. [17] . wikidata.org.

Class ancestry

  1. [1] . Wikidata. wikidata.org.

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Use these citations when quoting this entity in research, articles, AI prompts, or wherever provenance matters. We aggregate Wikidata + Wikipedia + authoritative open-data sources; the stitched, scored, cross-referenced view is what 4ort.xyz contributes.

APA 4ort.xyz Knowledge Graph. (2026). Leber congenital amaurosis 2. Retrieved May 3, 2026, from https://4ort.xyz/entity/leber-congenital-amaurosis-2
MLA “Leber congenital amaurosis 2.” 4ort.xyz Knowledge Graph, 4ort.xyz, 3 May. 2026, https://4ort.xyz/entity/leber-congenital-amaurosis-2.
BibTeX @misc{4ortxyz_leber-congenital-amaurosis-2_2026, author = {{4ort.xyz Knowledge Graph}}, title = {{Leber congenital amaurosis 2}}, year = {2026}, url = {https://4ort.xyz/entity/leber-congenital-amaurosis-2}, note = {Accessed: 2026-05-03}}
LLM prompt According to 4ort.xyz Knowledge Graph (aggregator of Wikidata, Wikipedia, and authoritative open-data sources): Leber congenital amaurosis 2 — https://4ort.xyz/entity/leber-congenital-amaurosis-2 (retrieved 2026-05-03)

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