IGSF1 deficiency syndrome

X-linked disease characterized by hypothyroidism that is present at birth, delayed testosterone increase in puberty, and testicular enlargement in adulthood that has material basis in mutation of the IGSF1 gene on chromosome Xq26
MedicalCondition class_of_disease Q50349806
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IGSF1 deficiency syndrome

Summary

IGSF1 deficiency syndrome is a class of disease[1].

Key Facts

  • IGSF1 deficiency syndrome's instance of is recorded as class of disease[2].
  • IGSF1 deficiency syndrome's subclass of is recorded as central congenital hypothyroidism[3].
  • IGSF1 deficiency syndrome's subclass of is recorded as X-linked recessive disease[4].
  • IGSF1 deficiency syndrome's subclass of is recorded as syndrome[5].
  • IGSF1 deficiency syndrome's OMIM ID is recorded as 300888[6].
  • IGSF1 deficiency syndrome's KEGG ID is recorded as H02034[7].
  • IGSF1 deficiency syndrome's Disease Ontology ID is recorded as DOID:0111140[8].
  • IGSF1 deficiency syndrome's Orphanet ID is recorded as 329235[9].
  • IGSF1 deficiency syndrome's genetic association is recorded as IGSF1[10].
  • IGSF1 deficiency syndrome's exact match is recorded as http://purl.obolibrary.org/obo/DOID_0111140[11].
  • IGSF1 deficiency syndrome's exact match is recorded as http://identifiers.org/doid/DOID:0111140[12].
  • IGSF1 deficiency syndrome's exact match is recorded as http://www.orpha.net/ORDO/Orphanet_329235[13].
  • IGSF1 deficiency syndrome's UMLS CUI is recorded as C3550963[14].
  • IGSF1 deficiency syndrome's UMLS CUI is recorded as C4749943[15].
  • IGSF1 deficiency syndrome's ICD-10-CM is recorded as E03.1[16].
  • IGSF1 deficiency syndrome's on focus list of Wikimedia project is recorded as WikiProject Medicine[17].
  • IGSF1 deficiency syndrome's Mondo ID is recorded as MONDO_0010475[18].
  • IGSF1 deficiency syndrome's UniProt disease ID is recorded as DI-03629[19].

References

Programmatic citations — every numbered marker resolves to a verifiable graph row below.

Direct Wikidata claims

  1. [2] ↑ . wikidata.org.
  2. [3] ↑ . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  3. [4] ↑ . Disease Ontology. Retrieved . wikidata.org.
  4. [5] ↑ . Disease Ontology. Retrieved . wikidata.org.
  5. [6] ↑ . Disease Ontology. Retrieved . wikidata.org.
  6. [7] ↑ . wikidata.org.
  7. [8] ↑ . Disease Ontology. Retrieved . wikidata.org.
  8. [9] ↑ . Disease Ontology. Retrieved . wikidata.org.
  9. [10] ↑ . Q905695. Retrieved . platform.opentargets.org. Provenance: wikidata.org.
  10. [11] ↑ . Disease Ontology. Retrieved . wikidata.org.
  11. [12] ↑ . Identifiers.org. registry.identifiers.org. Provenance: wikidata.org.
  12. [13] ↑ . wikidata.org.
  13. [14] ↑ . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  14. [15] ↑ . UMLS 2023. Retrieved . wikidata.org.
  15. [16] ↑ . Disease Ontology. Retrieved . wikidata.org.
  16. [17] ↑ . wikidata.org.
  17. [18] ↑ . wikidata.org.
  18. [19] ↑ . wikidata.org.

Class ancestry

  1. [1] ↑ . Wikidata. wikidata.org.

📑 Cite this page

Use these citations when quoting this entity in research, articles, AI prompts, or wherever provenance matters. We aggregate Wikidata + Wikipedia + authoritative open-data sources; the stitched, scored, cross-referenced view is what 4ort.xyz contributes.

APA 4ort.xyz Knowledge Graph. (2026). IGSF1 deficiency syndrome. Retrieved May 3, 2026, from https://4ort.xyz/entity/igsf1-deficiency-syndrome
MLA “IGSF1 deficiency syndrome.” 4ort.xyz Knowledge Graph, 4ort.xyz, 3 May. 2026, https://4ort.xyz/entity/igsf1-deficiency-syndrome.
BibTeX @misc{4ortxyz_igsf1-deficiency-syndrome_2026, author = {{4ort.xyz Knowledge Graph}}, title = {{IGSF1 deficiency syndrome}}, year = {2026}, url = {https://4ort.xyz/entity/igsf1-deficiency-syndrome}, note = {Accessed: 2026-05-03}}
LLM prompt According to 4ort.xyz Knowledge Graph (aggregator of Wikidata, Wikipedia, and authoritative open-data sources): IGSF1 deficiency syndrome — https://4ort.xyz/entity/igsf1-deficiency-syndrome (retrieved 2026-05-03)

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