Erdheim-Chester disease

rare disease
MedicalCondition class_of_disease Q1349259
Erdheim-Chester disease
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Erdheim-Chester disease

Summary

Erdheim-Chester disease is a class of disease[1]. It draws 261 Wikipedia views per month (class_of_disease category, ranking #399 of 1,968).[2]

Key Facts

  • Erdheim-Chester disease's image is recorded as Maladie de Chester-Erdheim.png[3].
  • Erdheim-Chester disease's instance of is recorded as class of disease[4].
  • Erdheim-Chester disease's subclass of is recorded as non-Langerhans-cell histiocytosis[5].
  • Erdheim-Chester disease's subclass of is recorded as granulomatous autoinflammatory syndrome[6].
  • Erdheim-Chester disease's subclass of is recorded as histiocytic and dendritic cell cancer[7].
  • Erdheim-Chester disease's subclass of is recorded as connective tissue neoplasm[8].
  • Erdheim-Chester disease's subclass of is recorded as immune disorder[9].
  • Erdheim-Chester disease's subclass of is recorded as disease[10].
  • Erdheim-Chester disease's Commons category is recorded as Erdheim–Chester disease[11].
  • Erdheim-Chester disease's MeSH descriptor ID is recorded as D031249[12].
  • Erdheim-Chester disease's ICD-9 ID is recorded as 202.3[13].
  • Erdheim-Chester disease's ICD-10 ID is recorded as C96.1[14].
  • Erdheim-Chester disease's DiseasesDB is recorded as 29792[15].
  • Erdheim-Chester disease's Freebase ID is recorded as /m/0gbvzt[16].
  • Erdheim-Chester disease's KEGG ID is recorded as H02425[17].
  • Erdheim-Chester disease's MeSH tree code is recorded as C15.604.250.410.224[18].
  • Erdheim-Chester disease's Disease Ontology ID is recorded as DOID:4329[19].
  • Erdheim-Chester disease's Orphanet ID is recorded as 35687[20].
  • Erdheim-Chester disease's ICD-9-CM is recorded as 277.89[21].
  • Erdheim-Chester disease's NCI Thesaurus ID is recorded as C53972[22].
  • Erdheim-Chester disease's health specialty is recorded as oncology[23].
  • Erdheim-Chester disease's health specialty is recorded as hematology[24].
  • Erdheim-Chester disease's drug or therapy used for treatment is recorded as vemurafenib[25].
  • Erdheim-Chester disease's drug or therapy used for treatment is recorded as cobimetinib[26].
  • Erdheim-Chester disease's BabelNet ID is recorded as 03504203n[27].

Why It Matters

Erdheim-Chester disease draws 261 Wikipedia views per month (class_of_disease category, ranking #399 of 1,968).[2] It has Wikipedia articles in 12 language editions, a strong signal of global cultural recognition.[28] It is known by 23 alternative names across languages and contexts.[29]

References

Programmatic citations — every numbered marker resolves to a verifiable graph row below.

Direct Wikidata claims

  1. [3] . wikidata.org.
  2. [4] . wikidata.org.
  3. [5] . Disease Ontology. Retrieved . wikidata.org.
  4. [6] . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  5. [7] . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  6. [8] . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  7. [9] . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  8. [10] . wikidata.org.
  9. [11] . wikidata.org.
  10. [12] . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  11. [13] . wikidata.org.
  12. [14] . wikidata.org.
  13. [15] . wikidata.org.
  14. [16] . Freebase Data Dumps. wikidata.org.
  15. [17] . wikidata.org.
  16. [18] . wikidata.org.
  17. [19] . Disease Ontology. Retrieved . wikidata.org.
  18. [20] . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  19. [21] . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  20. [22] . Disease Ontology. Retrieved . wikidata.org.
  21. [23] . wikidata.org.
  22. [24] . wikidata.org.
  23. [25] . Dramatic efficacy of vemurafenib in both multisystemic and refractory Erdheim-Chester disease and Langerhans cell histiocytosis harboring the BRAF V600E mutation. Retrieved . wikidata.org.
  24. [26] . onclive.com. onclive.com. Provenance: wikidata.org.
  25. [27] . BabelNet. wikidata.org.

Class ancestry

  1. [1] . Wikidata. wikidata.org.

Aggregate / graph-position facts

  1. [2] . Wikimedia Foundation. dumps.wikimedia.org.
  2. [28] . Wikidata sitelinks. wikidata.org.
  3. [29] . Wikidata aliases. wikidata.org.

📑 Cite this page

Use these citations when quoting this entity in research, articles, AI prompts, or wherever provenance matters. We aggregate Wikidata + Wikipedia + authoritative open-data sources; the stitched, scored, cross-referenced view is what 4ort.xyz contributes.

APA 4ort.xyz Knowledge Graph. (2026). Erdheim-Chester disease. Retrieved May 3, 2026, from https://4ort.xyz/entity/erdheim-chester-disease
MLA “Erdheim-Chester disease.” 4ort.xyz Knowledge Graph, 4ort.xyz, 3 May. 2026, https://4ort.xyz/entity/erdheim-chester-disease.
BibTeX @misc{4ortxyz_erdheim-chester-disease_2026, author = {{4ort.xyz Knowledge Graph}}, title = {{Erdheim-Chester disease}}, year = {2026}, url = {https://4ort.xyz/entity/erdheim-chester-disease}, note = {Accessed: 2026-05-03}}
LLM prompt According to 4ort.xyz Knowledge Graph (aggregator of Wikidata, Wikipedia, and authoritative open-data sources): Erdheim-Chester disease — https://4ort.xyz/entity/erdheim-chester-disease (retrieved 2026-05-03)

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