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Behçet's disease

rare immune-mediated small-vessel systemic vasculitis in humans
Class type of: vasculitis, secondary glomerular disease, rare skin disease Q911427

Facts

18 properties
Instance of
designated intractable/rare disease, class of disease[6]
Subclass of
vasculitis, secondary glomerular disease, rare skin disease, systemic diseases with anterior uveitis, systemic diseases with posterior uveitis, systemic diseases with panuveitis, autoinflammatory syndrome with skin involvement, vascular skin disease, unclassified autoinflammatory syndrome, predominantly large-vessel vasculitis, inflammatory and autoimmune disease with epilepsy, autoimmune disease of cardiovascular system[8][9][10][11][12][13][14][15]
Afflicts
blood vessel[16]
Age of onset
juvenile onset, adult onset, childhood onset
Drug or therapy used for treatment
thalidomide, apremilast, cyclosporine, etanercept, adalimumab, (S)-(−)-colchicine, infliximab[42][43][44][45][46][47][48]
Genetic association
STAT4, TFCP2L1, PSORS1C1, IL10, C4A, CCR1, HLA-B, IFNGR1, IL12A, KLRC4, MEFV, TLR4, FAS, ERAP1, IL23R, UBAC2, IL12A-AS1[49][50][51]
Has cause
immune system[31]
Has phenotype
uveitis, Nausea and vomiting, aphthous stomatitis, gait abnormality, abdominal pain, genital ulcer, Wikidata item, Abnormal blistering of the skin, cataract, seizure, abnormal reflex, pleurisy, pulmonary infiltrate, vertigo, memory disorder, encephalitis, lymphadenopathy, pyramidal sign, endocarditis, optic neuritis
Health specialty
immunology, rheumatology[40][41]
ICD-9-CM
136.1[38]
NCI Thesaurus ID
C34416[39]
Named after
Hulusi Behçet[7]
On focus list of Wikimedia project
WikiProject Medicine
P14541
1rm2K8
P14914
D00117
Possible treatment
corticosteroid, TNF inhibitor, interferon alpha 2, azathioprine, immunoglobulin therapy[32][33][34][35][36]
Prevalence
+0.00005[37]
Symptoms and signs
aphthous stomatitis, ulceration of vulva, erythema nodosum, cutaneous pustular vasculitis, uveitis, retinal vasculitis, Hypopyon, abdominal pain, nausea, diarrhea, hemoptysis, pleurisy, cough, fever, arthritis, meningoencephalitis, aseptic meningitis, pericarditis, pathergy, acne, chronic widespread pain, inflammation[17][18][19][20][21][22][23][24][25][26][27][28][29][30]
🏷️ Also known as
en Behçet's syndrome en Behcet's syndrome en Behçet’s Syndrome en Behçet's Syndrome en Behcet syndrome en Behçet syndrome en Morbus Behçet's Syndrome en Morbus Behçet en triple symptom complex en Silk Road disease en Morbus Behcet en Adamantiades-Behcet disease en Adamantiades-Behçet disease en Bechet syndrome en Behçet-Adamantiades Syndrome en Behcet disease en Behcet Disease en Behçet disease en Behcet's disease en Behçet's disease
🔖 Identifiers · 30
OpenAlex ID
C2781428731, C3018415437
Image (Wikimedia Commons)
Behcets disease.jpg ↗
Disease Ontology ID
DOID:13241
DiseasesDB
1285
EMedicine ID
1.2M (1.0M–1.2M, n=3)
Encyclopedia of China (Third Edition) ID
298161
Exact match
purl.obolibrary.org, identifiers.org, www.orpha.net
External data available at URL
www.nanbyou.or.jp
Freebase ID
/m/025t67z
GARD rare disease ID
848
Gran Enciclopèdia Catalana ID
sindrome-de-behcet
Gran Enciclopèdia Catalana ID (former scheme)
0008651
Show all 30 identifiers +18
ICD-10-CM
M35.2
ICD-11 ID (Foundation)
1668927157
ICD-11 ID (MMS)
4A62
KEGG ID
H01476
Lex ID
Behcets_sygdom
MeSH descriptor ID
D001528
MeSH tree code
C07.465.075, C11.941.879.780.880.200, C14.907.940.100, C16.320.382.250, C17.800.827.368.250, C17.800.862.150
Mondo ID
MONDO_0007191
NDL Authority ID
00560569
NHS Health A to Z ID
behcets-disease
Namuwiki ID
베체트병
OMIM ID
109650
Orphanet ID
117
PatientsLikeMe condition ID
behcet-s-disease
Store medisinske leksikon ID
Behçets_syndrom
Subreddit
Behcets
UMLS CUI
C0004943
WikiProjectMed ID
Behçet's disease

Report an error or request removal Lineage (PROV-JSON)

⛏️ Lake Facts · open-dataset statements via 4ort-mint

From open datasets, joined by identifier and shown only for properties Wikidata does not state on this entity — except where the dataset is the registry authority for the fact (ClinicalTrials.gov on trial registration data): there its value is shown instead, with Wikidata's noted beside it. Every row carries its dataset edition and licence.

Library of Congress authority IDP244
sh85012908 2026-10-01 ndl_authorities (pdl-1.0) as of 2026-10-01
where from?
Source
ndl_authorities
Edition
20261001 · as of 2026-10-01 · newer edition 20261103 landed
Licence
pdl-1.0
Credit
data obtained from Web NDL Authorities (National Diet Library)
Bronze
manifest sha256 6e048898660f1188…
Transform
4ort-mint · lake · version not recorded
data obtained from Web NDL Authorities (National Diet Library)
🔗 Connections
Symptoms and signs 18
fever, diarrhea, cough, acne, inflammation, arthritis, nausea, abdominal pain +10 more
Drug or therapy used for treatment 7
thalidomide, (S)-(−)-colchicine, cyclosporine, infliximab, adalimumab, etanercept, apremilast
← Medical condition treated 7
thalidomide, (S)-(−)-colchicine, cyclosporine, infliximab, adalimumab, etanercept, apremilast
Possible treatment 4
corticosteroid, azathioprine, immunoglobulin therapy, TNF inhibitor
Health specialty 2
immunology, rheumatology
Subclass of 2
disease, vasculitis
Afflicts 1
blood vessel
Genetic association 1
STAT4
Has cause 1
immune system
Has phenotype 1
uveitis
Named after 1
Hulusi Behçet
On focus list of Wikimedia project 1
WikiProject Medicine
← Genetic association 1
STAT4
← Suggests the existence of 1
hemoptysis
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Summary

Behçet's disease is a designated intractable/rare disease[1]. It is a type of vasculitis[2], secondary glomerular disease[3], rare skin disease[4], and systemic diseases with anterior uveitis[5].

Related Entities

disease immunology rheumatology

References

Programmatic citations — every numbered marker resolves to a verifiable graph row below.

Direct Wikidata claims

  1. [6] ↑ . wikidata.org.
  2. [7] ↑ . wikidata.org.
  3. [2] ↑ . Disease Ontology. Retrieved . wikidata.org.
  4. [3] ↑ . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  5. [4] ↑ . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  6. [5] ↑ . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  7. [8] ↑ . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  8. [9] ↑ . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  9. [10] ↑ . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  10. [11] ↑ . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  11. [12] ↑ . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  12. [13] ↑ . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  13. [14] ↑ . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  14. [15] ↑ . Disease Ontology. Retrieved . wikidata.org.
  15. [16] ↑ . wikidata.org.
  16. [17] ↑ . worldcat.org. worldcat.org. Provenance: wikidata.org.
  17. [18] ↑ . worldcat.org. worldcat.org. Provenance: wikidata.org.
  18. [19] ↑ . worldcat.org. worldcat.org. Provenance: wikidata.org.
  19. [20] ↑ . worldcat.org. worldcat.org. Provenance: wikidata.org.
  20. [21] ↑ . worldcat.org. worldcat.org. Provenance: wikidata.org.
  21. [22] ↑ . worldcat.org. worldcat.org. Provenance: wikidata.org.
  22. [23] ↑ . worldcat.org. worldcat.org. Provenance: wikidata.org.
  23. [24] ↑ . worldcat.org. worldcat.org. Provenance: wikidata.org.
  24. [25] ↑ . worldcat.org. worldcat.org. Provenance: wikidata.org.
  25. [26] ↑ . worldcat.org. worldcat.org. Provenance: wikidata.org.
  26. [27] ↑ . worldcat.org. worldcat.org. Provenance: wikidata.org.
  27. [28] ↑ . worldcat.org. worldcat.org. Provenance: wikidata.org.
  28. [29] ↑ . worldcat.org. worldcat.org. Provenance: wikidata.org.
  29. [30] ↑ . worldcat.org. worldcat.org. Provenance: wikidata.org.
  30. [31] ↑ . wikidata.org.
  31. [32] ↑ . ncbi.nlm.nih.gov. ncbi.nlm.nih.gov. Provenance: wikidata.org.
  32. [33] ↑ . Effect of infliximab on sight-threatening panuveitis in Behçet's disease. wikidata.org.
  33. [34] ↑ . Interferon alfa-2a in the treatment of Behçet disease: a randomized placebo-controlled and double-blind study. wikidata.org.
  34. [35] ↑ . wikidata.org.
  35. [36] ↑ . wikidata.org.
  36. [37] ↑ . Retrieved . wikidata.org.
  37. [38] ↑ . Disease Ontology. Retrieved . wikidata.org.
  38. [39] ↑ . Disease Ontology. Retrieved . wikidata.org.
  39. [40] ↑ . wikidata.org.
  40. [41] ↑ . wikidata.org.
  41. [42] ↑ . NDF-RT. Retrieved . wikidata.org.
  42. [43] ↑ . Drug Indications Extracted from FAERS. Retrieved . wikidata.org.
  43. [44] ↑ . Drug Indications Extracted from FAERS. Retrieved . wikidata.org.
  44. [45] ↑ . Drug Indications Extracted from FAERS. Retrieved . wikidata.org.
  45. [46] ↑ . Drug Indications Extracted from FAERS. Retrieved . wikidata.org.
  46. [47] ↑ . Drug Indications Extracted from FAERS. Retrieved . wikidata.org.
  47. [48] ↑ . Drug Indications Extracted from FAERS. Retrieved . wikidata.org.
  48. [49] ↑ . Phenocarta. Retrieved . gemma.msl.ubc.ca. Provenance: wikidata.org.
  49. [50] ↑ . Phenocarta. Retrieved . gemma.msl.ubc.ca. Provenance: wikidata.org.
  50. [51] ↑ . Phenocarta. Retrieved . gemma.msl.ubc.ca. Provenance: wikidata.org.

Class ancestry

  1. [1] ↑ . Wikidata. wikidata.org.

📑 Cite this page

Use these citations when quoting this entity in research, articles, AI prompts, or wherever provenance matters. We aggregate Wikidata + Wikipedia + authoritative open-data sources; the stitched, scored, cross-referenced view is what 4ort.xyz contributes.

APA 4ort.xyz Knowledge Graph. (2026). Behçet's disease. Retrieved November 4, 2026, from https://4ort.xyz/entity/beh-et-s-disease
MLA “Behçet's disease.” 4ort.xyz Knowledge Graph, 4ort.xyz, 4 Nov. 2026, https://4ort.xyz/entity/beh-et-s-disease.
BibTeX @misc{4ortxyz_beh-et-s-disease_2026, author = {{4ort.xyz Knowledge Graph}}, title = {{Behçet's disease}}, year = {2026}, url = {https://4ort.xyz/entity/beh-et-s-disease}, note = {Accessed: 2026-11-04}}
LLM prompt According to 4ort.xyz Knowledge Graph (aggregator of Wikidata, Wikipedia, and authoritative open-data sources): Behçet's disease — https://4ort.xyz/entity/beh-et-s-disease (retrieved 2026-11-04)

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Edit History

Rolling log of changes to this entity's Wikidata record. Values shown reflect the current state of each edited property — follow the history link to see the precise diff for any edit.

  1. 12d ago · ACorrêa (WMB) · 2026-10-23 view diff on Wikidata ↗
    Genetic association → STAT4, TFCP2L1, PSORS1C1 +14
    Sitelink count → 34
    Prevalence → {'amount': '+0.00005'}
    Wikipedia languages → ['ar', 'az', 'azb', 'bg', 'ca', 'ckb', 'commons', 'de', 'el', 'en', 'es', 'fa',
    + 4 other properties edited (see Wikidata diff for full list)
    "/* wbeditentity-update:0| */ QuickStatements 3.0 [[:toollabs:qs-dev/batch/61469|batch #61469]]: Raras.org data import"
  2. 16w ago · Nyuhn · 2026-07-10 view diff on Wikidata ↗
    P14541 → 1rm2K8
    "/* wbeditentity-update:0| */ QuickStatements 3.0 [[:toollabs:qs-dev/batch/40849|batch #40849]]: ZGBK ID"
  3. 17w ago · JhealdBatch bot · 2026-07-03 view diff on Wikidata ↗
    Subclass of → vasculitis, secondary glomerular disease, rare skin disease +9
    On focus list of Wikimedia project → WikiProject Medicine
    Named after → —
    Possible treatment → corticosteroid, TNF inhibitor, interferon alpha 2 +2
    + 12 other properties edited (see Wikidata diff for full list)
    "/* wbeditentity-update:0| */ QuickStatements 3.0 [[:toollabs:qs-dev/batch/39732|batch #39732]]: rm redundant subclass"
Live feed via Wikidata EventStreams. New edits appear within minutes of being made on Wikidata.