AL amyloidosis
medical condition
Facts
8 properties- Instance of
- designated intractable/rare disease, class of disease[2]
- Subclass of
- amyloidosis, plasma cell neoplasm, lymphoproliferative disorders, paraproteinemia[3][4][5][6]
- Age of onset
- adult onset[10]
- Has phenotype
- fatigue, kidney disease, nephrotic syndrome, congenital heart disease, hypertrophic cardiomyopathy, malabsorption, interstitial lung disease, hypergammaglobulinemia, Wikidata item, Wikidata item, kidney failure, xerostomia, elevated alkaline phosphatase, Wikidata item, salivary gland disease, peripheral edema, Wikidata item, Jaw claudication, dry cough, Howell–Jolly body, macroglossia, dysphonia, dysphagia, gastroparesis[11][12][13][14][15][16][17][18][19][20][21][22][23][24]
- Health specialty
- endocrinology[9]
- NCI Thesaurus ID
- C158963[8]
- P14914
- D85443[25]
- Prevalence
- +0.00005[7]
🏷️ Also known as
en Light-chain amyloidosis
en Primary amyloidosis
en Systemic amyloidosis
en AL amyloidosis
en immunoglobulin light-chain amyloidosis
da AL Amyloidose
da Amyloid Let-kæde amyloidose
de AL-Amyloidose
fr amylose AL
fr amylose primitive
it Amiloidosi AL
ja 全身性ALアミロイドーシス
sv AL-amyloidos
zh 初級類澱粉症
🔖 Identifiers · 23
- OpenAlex ID
- C2779551797, C2780945303
- BabelNet ID
- 01017975n
- DiseasesDB
- 315
- EMedicine ID
- 208839
- Exact match
- www.orpha.net
- External data available at URL
- www.nanbyou.or.jp
- GARD rare disease ID
- 5797
- ICD-10 ID
- E85
- ICD-10-CM
- E85.9
- ICD-11 ID (Foundation)
- 1061366491
- ICD-11 ID (MMS)
- 5D00.0
- ICD-9 ID
- 277.3
Show all 23 identifiers +11
- ICD-O
- 9769/1
- MeSH descriptor ID
- D000075363
- MeSH tree code
- C04.557.595.250, C18.452.845.500.550, C20.683.515.507, C20.683.780.565
- Medical Dictionary for Regulatory Activities ID
- 10002022
- MedlinePlus ID
- 000533
- Microsoft Academic ID (discontinued)
- 2.9B (2.8B–2.9B, n=3)
- Mondo ID
- MONDO_0019438
- OMIM ID
- 254500
- Orphanet ID
- 85443
- UMLS CUI
- C0268381
- WikiProjectMed ID
- AL amyloidosis
🔗 Connections
Subclass of 3
Health specialty 1
← Cause of death 1
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Summary
AL amyloidosis is a designated intractable/rare disease[1].