agammaglobulinemia

B cell deficiency that is caused by a reduction in all types of gamma globulins
MedicalCondition rare_disease Q1047559
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agammaglobulinemia

Summary

agammaglobulinemia is a rare disease[1]. agammaglobulinemia draws 117 Wikipedia views per month (rare_disease category, ranking #153 of 627).[2]

Key Facts

  • agammaglobulinemia's instance of is recorded as rare disease[3].
  • agammaglobulinemia's instance of is recorded as class of disease[4].
  • agammaglobulinemia's subclass of is recorded as B cell deficiency[5].
  • agammaglobulinemia's subclass of is recorded as immunodeficiency predominantly affecting antibody production[6].
  • agammaglobulinemia's OMIM ID is recorded as 601495[7].
  • agammaglobulinemia's OMIM ID is recorded as 612692[8].
  • agammaglobulinemia's OMIM ID is recorded as 613500[9].
  • agammaglobulinemia's OMIM ID is recorded as 613501[10].
  • agammaglobulinemia's OMIM ID is recorded as 613502[11].
  • agammaglobulinemia's OMIM ID is recorded as 613506[12].
  • agammaglobulinemia's OMIM ID is recorded as 615214[13].
  • agammaglobulinemia's DiseasesDB is recorded as 6426[14].
  • agammaglobulinemia's MedlinePlus ID is recorded as 001307[15].
  • agammaglobulinemia's eMedicine ID is recorded as 884942[16].
  • agammaglobulinemia's Disease Ontology ID is recorded as DOID:2583[17].
  • agammaglobulinemia's Encyclopædia Britannica Online ID is recorded as science/hypogammaglobulinemia[18].
  • agammaglobulinemia's Patientplus ID is recorded as Hypogammaglobulinaemia[19].
  • agammaglobulinemia's Orphanet ID is recorded as 183669[20].
  • agammaglobulinemia's ICD-9-CM is recorded as 279.00[21].
  • agammaglobulinemia's NCI Thesaurus ID is recorded as C26931[22].
  • agammaglobulinemia's different from is recorded as agammaglobulinemia[23].
  • agammaglobulinemia's health specialty is recorded as hematology[24].
  • agammaglobulinemia's genetic association is recorded as CD79B[25].
  • agammaglobulinemia's genetic association is recorded as PIK3R1[26].
  • agammaglobulinemia's genetic association is recorded as CD79A[27].

Why It Matters

agammaglobulinemia draws 117 Wikipedia views per month (rare_disease category, ranking #153 of 627).[2] agammaglobulinemia has Wikipedia articles in 7 language editions, a strong signal of global cultural recognition.[28] agammaglobulinemia is known by 8 alternative names across languages and contexts.[29]

References

Programmatic citations — every numbered marker resolves to a verifiable graph row below.

Direct Wikidata claims

  1. [3] . wikidata.org.
  2. [4] . wikidata.org.
  3. [5] . Disease Ontology. Retrieved . wikidata.org.
  4. [6] . wikidata.org.
  5. [7] . Disease Ontology. Retrieved . wikidata.org.
  6. [8] . Disease Ontology. Retrieved . wikidata.org.
  7. [9] . Disease Ontology. Retrieved . wikidata.org.
  8. [10] . Disease Ontology. Retrieved . wikidata.org.
  9. [11] . Disease Ontology. Retrieved . wikidata.org.
  10. [12] . Disease Ontology. Retrieved . wikidata.org.
  11. [13] . Disease Ontology. Retrieved . wikidata.org.
  12. [14] . wikidata.org.
  13. [15] . wikidata.org.
  14. [16] . wikidata.org.
  15. [17] . Disease Ontology. Retrieved . wikidata.org.
  16. [18] . wikidata.org.
  17. [19] . patient.co.uk. patient.co.uk. Provenance: wikidata.org.
  18. [20] . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  19. [21] . Disease Ontology. Retrieved . wikidata.org.
  20. [22] . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  21. [23] . wikidata.org.
  22. [24] . wikidata.org.
  23. [25] . Cutting edge: a hypomorphic mutation in Igbeta (CD79b) in a patient with immunodeficiency and a leaky defect in B cell development. wikidata.org.
  24. [26] . Agammaglobulinemia and absent B lineage cells in a patient lacking the p85α subunit of PI3K.. wikidata.org.
  25. [27] . Mutations in Igalpha (CD79a) result in a complete block in B-cell development. wikidata.org.

Class ancestry

  1. [1] . Wikidata. wikidata.org.

Aggregate / graph-position facts

  1. [2] . Wikimedia Foundation. dumps.wikimedia.org.
  2. [28] . Wikidata sitelinks. wikidata.org.
  3. [29] . Wikidata aliases. wikidata.org.

📑 Cite this page

Use these citations when quoting this entity in research, articles, AI prompts, or wherever provenance matters. We aggregate Wikidata + Wikipedia + authoritative open-data sources; the stitched, scored, cross-referenced view is what 4ort.xyz contributes.

APA 4ort.xyz Knowledge Graph. (2026). agammaglobulinemia. Retrieved May 3, 2026, from https://4ort.xyz/entity/agammaglobulinemia
MLA “agammaglobulinemia.” 4ort.xyz Knowledge Graph, 4ort.xyz, 3 May. 2026, https://4ort.xyz/entity/agammaglobulinemia.
BibTeX @misc{4ortxyz_agammaglobulinemia_2026, author = {{4ort.xyz Knowledge Graph}}, title = {{agammaglobulinemia}}, year = {2026}, url = {https://4ort.xyz/entity/agammaglobulinemia}, note = {Accessed: 2026-05-03}}
LLM prompt According to 4ort.xyz Knowledge Graph (aggregator of Wikidata, Wikipedia, and authoritative open-data sources): agammaglobulinemia — https://4ort.xyz/entity/agammaglobulinemia (retrieved 2026-05-03)

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