Aagenaes syndrome

syndrome that is characterized by congenital hypoplasia of lymph vessels, which causes lymphedema of the legs and recurrent cholestasis in infancy, and slow progress to hepatic cirrhosis and giant cell hepatitis with fibrosis of the portal tracts
MedicalCondition class_of_disease Q300801
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Aagenaes syndrome

Summary

Aagenaes syndrome is a class of disease[1]. It draws 31 Wikipedia views per month (class_of_disease category, ranking #608 of 1,968).[2]

Key Facts

  • Aagenaes syndrome's image is recorded as Primary intestinal lymphangiectasia (Waldmann's disease) - legs.jpg[3].
  • Aagenaes syndrome's instance of is recorded as class of disease[4].
  • Aagenaes syndrome's subclass of is recorded as syndrome[5].
  • Aagenaes syndrome's subclass of is recorded as primary lymphedema with associated anomalies[6].
  • Aagenaes syndrome's subclass of is recorded as genetic vascular anomaly[7].
  • Aagenaes syndrome's subclass of is recorded as rare genetic hepatic disease[8].
  • Aagenaes syndrome's subclass of is recorded as syndromic lymphedema[9].
  • Aagenaes syndrome's subclass of is recorded as rare genetic immune disease[10].
  • Aagenaes syndrome's subclass of is recorded as disease[11].
  • Aagenaes syndrome's Commons category is recorded as Aagenaes syndrome[12].
  • Aagenaes syndrome's MeSH descriptor ID is recorded as C535330[13].
  • Aagenaes syndrome's OMIM ID is recorded as 214900[14].
  • Aagenaes syndrome's DiseasesDB is recorded as 32129[15].
  • Aagenaes syndrome's Freebase ID is recorded as /m/03k5c2[16].
  • Aagenaes syndrome's Disease Ontology ID is recorded as DOID:6691[17].
  • Aagenaes syndrome's symptoms and signs is recorded as hepatitis[18].
  • Aagenaes syndrome's Orphanet ID is recorded as 1414[19].
  • Aagenaes syndrome's ICD-9-CM is recorded as 576.8[20].
  • Aagenaes syndrome's NCI Thesaurus ID is recorded as C35709[21].
  • Aagenaes syndrome's exact match is recorded as http://purl.obolibrary.org/obo/DOID_6691[22].
  • Aagenaes syndrome's exact match is recorded as http://identifiers.org/doid/DOID:6691[23].
  • Aagenaes syndrome's UMLS CUI is recorded as C0268314[24].
  • Aagenaes syndrome's ICD-10-CM is recorded as Q82.0[25].
  • Aagenaes syndrome's GARD rare disease ID is recorded as 370[26].
  • Aagenaes syndrome's on focus list of Wikimedia project is recorded as WikiProject Medicine[27].

Why It Matters

Aagenaes syndrome draws 31 Wikipedia views per month (class_of_disease category, ranking #608 of 1,968).[2] It has Wikipedia articles in 12 language editions, a strong signal of global cultural recognition.[28] It is known by 21 alternative names across languages and contexts.[29]

References

Programmatic citations — every numbered marker resolves to a verifiable graph row below.

Direct Wikidata claims

  1. [3] . wikidata.org.
  2. [4] . wikidata.org.
  3. [5] . Disease Ontology. Retrieved . wikidata.org.
  4. [6] . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  5. [7] . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  6. [8] . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  7. [9] . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  8. [10] . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  9. [11] . wikidata.org.
  10. [12] . wikidata.org.
  11. [13] . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  12. [14] . Disease Ontology. Retrieved . wikidata.org.
  13. [15] . wikidata.org.
  14. [16] . Freebase Data Dumps. wikidata.org.
  15. [17] . Disease Ontology. Retrieved . wikidata.org.
  16. [18] . Disease Ontology. Retrieved . wikidata.org.
  17. [19] . Disease Ontology. Retrieved . wikidata.org.
  18. [20] . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  19. [21] . Disease Ontology. Retrieved . wikidata.org.
  20. [22] . Disease Ontology. Retrieved . wikidata.org.
  21. [23] . Identifiers.org. registry.identifiers.org. Provenance: wikidata.org.
  22. [24] . Disease Ontology. Retrieved . wikidata.org.
  23. [25] . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  24. [26] . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  25. [27] . wikidata.org.

Class ancestry

  1. [1] . Wikidata. wikidata.org.

Aggregate / graph-position facts

  1. [2] . Wikimedia Foundation. dumps.wikimedia.org.
  2. [28] . Wikidata sitelinks. wikidata.org.
  3. [29] . Wikidata aliases. wikidata.org.

📑 Cite this page

Use these citations when quoting this entity in research, articles, AI prompts, or wherever provenance matters. We aggregate Wikidata + Wikipedia + authoritative open-data sources; the stitched, scored, cross-referenced view is what 4ort.xyz contributes.

APA 4ort.xyz Knowledge Graph. (2026). Aagenaes syndrome. Retrieved May 3, 2026, from https://4ort.xyz/entity/aagenaes-syndrome
MLA “Aagenaes syndrome.” 4ort.xyz Knowledge Graph, 4ort.xyz, 3 May. 2026, https://4ort.xyz/entity/aagenaes-syndrome.
BibTeX @misc{4ortxyz_aagenaes-syndrome_2026, author = {{4ort.xyz Knowledge Graph}}, title = {{Aagenaes syndrome}}, year = {2026}, url = {https://4ort.xyz/entity/aagenaes-syndrome}, note = {Accessed: 2026-05-03}}
LLM prompt According to 4ort.xyz Knowledge Graph (aggregator of Wikidata, Wikipedia, and authoritative open-data sources): Aagenaes syndrome — https://4ort.xyz/entity/aagenaes-syndrome (retrieved 2026-05-03)

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