Aagenaes syndrome

syndrome that is characterized by congenital hypoplasia of lymph vessels, which causes lymphedema of the legs and recurrent cholestasis in infancy, and slow progress to hepatic cirrhosis and giant cell hepatitis with fibrosis of the portal tracts
MedicalCondition class_of_disease Q300801
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Aagenaes syndrome

Summary

Aagenaes syndrome is a class of disease[1]. It has Wikipedia articles in 12 language editions, a strong signal of global cultural recognition.[2]

Key Facts

  • Aagenaes syndrome's instance of is recorded as class of disease[3].
  • Aagenaes syndrome is a type of syndrome[4].
  • Aagenaes syndrome is a type of primary lymphedema with associated anomalies[5].
  • Aagenaes syndrome is a type of genetic vascular anomaly[6].
  • Aagenaes syndrome is a type of rare genetic hepatic disease[7].
  • Aagenaes syndrome is a type of syndromic lymphedema[8].
  • Aagenaes syndrome is a type of rare genetic immune disease[9].
  • Aagenaes syndrome is a type of disease[10].
  • Aagenaes syndrome's Commons category is recorded as Aagenaes syndrome[11].
  • Aagenaes syndrome's symptoms and signs is recorded as hepatitis[12].
  • Aagenaes syndrome's ICD-9-CM is recorded as 576.8[13].
  • Aagenaes syndrome's NCI Thesaurus ID is recorded as C35709[14].
  • Aagenaes syndrome's exact match is recorded as http://purl.obolibrary.org/obo/DOID_6691[15].
  • Aagenaes syndrome's exact match is recorded as http://identifiers.org/doid/DOID:6691[16].
  • Aagenaes syndrome's on focus list of Wikimedia project is recorded as WikiProject Medicine[17].
  • Aagenaes syndrome's has phenotype is recorded as liver cirrhosis[18].
  • Aagenaes syndrome's has phenotype is recorded as cholestasis[19].

Why It Matters

Aagenaes syndrome has Wikipedia articles in 12 language editions, a strong signal of global cultural recognition.[2] It is known by 21 alternative names across languages and contexts.[20]

References

Programmatic citations — every numbered marker resolves to a verifiable graph row below.

Direct Wikidata claims

  1. [3] . wikidata.org.
  2. [4] . Disease Ontology. Retrieved . wikidata.org.
  3. [5] . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  4. [6] . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  5. [7] . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  6. [8] . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  7. [9] . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  8. [10] . wikidata.org.
  9. [11] . wikidata.org.
  10. [12] . Disease Ontology. Retrieved . wikidata.org.
  11. [13] . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  12. [14] . Disease Ontology. Retrieved . wikidata.org.
  13. [15] . Disease Ontology. Retrieved . wikidata.org.
  14. [16] . Identifiers.org. registry.identifiers.org. Provenance: wikidata.org.
  15. [17] . wikidata.org.
  16. [18] . Disease Ontology. Retrieved . wikidata.org.
  17. [19] . Disease Ontology. Retrieved . wikidata.org.

Class ancestry

  1. [1] . Wikidata. wikidata.org.

Aggregate / graph-position facts

  1. [2] . Wikidata sitelinks. wikidata.org.
  2. [20] . Wikidata aliases. wikidata.org.

📑 Cite this page

Use these citations when quoting this entity in research, articles, AI prompts, or wherever provenance matters. We aggregate Wikidata + Wikipedia + authoritative open-data sources; the stitched, scored, cross-referenced view is what 4ort.xyz contributes.

APA 4ort.xyz Knowledge Graph. (2026). Aagenaes syndrome. Retrieved May 3, 2026, from https://4ort.xyz/entity/aagenaes-syndrome
MLA “Aagenaes syndrome.” 4ort.xyz Knowledge Graph, 4ort.xyz, 3 May. 2026, https://4ort.xyz/entity/aagenaes-syndrome.
BibTeX @misc{4ortxyz_aagenaes-syndrome_2026, author = {{4ort.xyz Knowledge Graph}}, title = {{Aagenaes syndrome}}, year = {2026}, url = {https://4ort.xyz/entity/aagenaes-syndrome}, note = {Accessed: 2026-05-03}}
LLM prompt According to 4ort.xyz Knowledge Graph (aggregator of Wikidata, Wikipedia, and authoritative open-data sources): Aagenaes syndrome — https://4ort.xyz/entity/aagenaes-syndrome (retrieved 2026-05-03)

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Edit History

Rolling log of changes to this entity's Wikidata record. Values shown reflect the current state of each edited property — follow the history link to see the precise diff for any edit.

  1. 22d ago · JhealdBatch bot · 2026-07-03 view diff on Wikidata ↗
    On focus list of wikimedia project WikiProject Medicine
    Has phenotype liver cirrhosis, cholestasis
    Subclass of
    Instance of class of disease
    + 4 other properties edited (see Wikidata diff for full list)
    "/* wbeditentity-update:0| */ QuickStatements 3.0 [[:toollabs:qs-dev/batch/39732|batch #39732]]: rm redundant subclass"
Live feed via Wikidata EventStreams. New edits appear within minutes of being made on Wikidata.