2-hydroxyglutaric aciduria

amino acid metabolic disorder that is an autosomal recessive neurometabolic disorder characterized by the significant elevation of urinary levels of hydroxyglutaric acid causing progressive brain damage
MedicalCondition class_of_disease Q4596888
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2-hydroxyglutaric aciduria

Summary

2-hydroxyglutaric aciduria is a class of disease[1]. It draws 7 Wikipedia views per month (class_of_disease category, ranking #629 of 1,968).[2]

Key Facts

  • 2-hydroxyglutaric aciduria's instance of is recorded as class of disease[3].
  • 2-hydroxyglutaric aciduria's subclass of is recorded as amino acid metabolic disorder[4].
  • 2-hydroxyglutaric aciduria's subclass of is recorded as neurometabolic disease[5].
  • 2-hydroxyglutaric aciduria's subclass of is recorded as cerebral organic aciduria[6].
  • 2-hydroxyglutaric aciduria's subclass of is recorded as rare genetic epilepsy[7].
  • 2-hydroxyglutaric aciduria's subclass of is recorded as amino acid or protein metabolism disease with epilepsy[8].
  • 2-hydroxyglutaric aciduria's OMIM ID is recorded as 600721[9].
  • 2-hydroxyglutaric aciduria's DiseasesDB is recorded as 34515[10].
  • 2-hydroxyglutaric aciduria's DiseasesDB is recorded as 34514[11].
  • 2-hydroxyglutaric aciduria's Disease Ontology ID is recorded as DOID:0050573[12].
  • 2-hydroxyglutaric aciduria's Orphanet ID is recorded as 19[13].
  • 2-hydroxyglutaric aciduria's ICD-9-CM is recorded as 270.8[14].
  • 2-hydroxyglutaric aciduria's NCI Thesaurus ID is recorded as C128187[15].
  • 2-hydroxyglutaric aciduria's exact match is recorded as http://purl.obolibrary.org/obo/DOID_0050573[16].
  • 2-hydroxyglutaric aciduria's exact match is recorded as http://identifiers.org/doid/DOID:0050573[17].
  • 2-hydroxyglutaric aciduria's exact match is recorded as http://www.orpha.net/ORDO/Orphanet_19[18].
  • 2-hydroxyglutaric aciduria's UMLS CUI is recorded as C2746066[19].
  • 2-hydroxyglutaric aciduria's ICD-10-CM is recorded as E72.8[20].
  • 2-hydroxyglutaric aciduria's GARD rare disease ID is recorded as 10761[21].
  • 2-hydroxyglutaric aciduria's on focus list of Wikimedia project is recorded as WikiProject Medicine[22].
  • 2-hydroxyglutaric aciduria's Mondo ID is recorded as MONDO_0016001[23].
  • 2-hydroxyglutaric aciduria's SNOMED CT ID is recorded as 698870008[24].
  • 2-hydroxyglutaric aciduria's Microsoft Academic ID is recorded as 2777654450[25].
  • 2-hydroxyglutaric aciduria's WikiProjectMed ID is recorded as 2-Hydroxyglutaric aciduria[26].

Why It Matters

2-hydroxyglutaric aciduria draws 7 Wikipedia views per month (class_of_disease category, ranking #629 of 1,968).[2]

References

Programmatic citations — every numbered marker resolves to a verifiable graph row below.

Direct Wikidata claims

  1. [3] . wikidata.org.
  2. [4] . Disease Ontology. Retrieved . wikidata.org.
  3. [5] . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  4. [6] . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  5. [7] . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  6. [8] . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  7. [9] . wikidata.org.
  8. [10] . wikidata.org.
  9. [11] . wikidata.org.
  10. [12] . Disease Ontology. Retrieved . wikidata.org.
  11. [13] . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  12. [14] . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  13. [15] . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  14. [16] . Disease Ontology. Retrieved . wikidata.org.
  15. [17] . Identifiers.org. registry.identifiers.org. Provenance: wikidata.org.
  16. [18] . wikidata.org.
  17. [19] . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  18. [20] . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  19. [21] . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  20. [22] . wikidata.org.
  21. [23] . wikidata.org.
  22. [24] . wikidata.org.
  23. [25] . wikidata.org.
  24. [26] . wikidata.org.

Class ancestry

  1. [1] . Wikidata. wikidata.org.

Aggregate / graph-position facts

  1. [2] . Wikimedia Foundation. dumps.wikimedia.org.

📑 Cite this page

Use these citations when quoting this entity in research, articles, AI prompts, or wherever provenance matters. We aggregate Wikidata + Wikipedia + authoritative open-data sources; the stitched, scored, cross-referenced view is what 4ort.xyz contributes.

APA 4ort.xyz Knowledge Graph. (2026). 2-hydroxyglutaric aciduria. Retrieved May 3, 2026, from https://4ort.xyz/entity/2-hydroxyglutaric-aciduria
MLA “2-hydroxyglutaric aciduria.” 4ort.xyz Knowledge Graph, 4ort.xyz, 3 May. 2026, https://4ort.xyz/entity/2-hydroxyglutaric-aciduria.
BibTeX @misc{4ortxyz_2-hydroxyglutaric-aciduria_2026, author = {{4ort.xyz Knowledge Graph}}, title = {{2-hydroxyglutaric aciduria}}, year = {2026}, url = {https://4ort.xyz/entity/2-hydroxyglutaric-aciduria}, note = {Accessed: 2026-05-03}}
LLM prompt According to 4ort.xyz Knowledge Graph (aggregator of Wikidata, Wikipedia, and authoritative open-data sources): 2-hydroxyglutaric aciduria — https://4ort.xyz/entity/2-hydroxyglutaric-aciduria (retrieved 2026-05-03)

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