spondylometaphyseal dysplasia, Kozlowski type

disease characterized by short stature (short-trunk dwarfism), scoliosis, metaphyseal abnormalities in the femur (prominent in the femoral neck and trochanteric area), coxa vara and generalized platyspondyly
MedicalCondition genetic_disease Q11695513
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spondylometaphyseal dysplasia, Kozlowski type

Summary

spondylometaphyseal dysplasia, Kozlowski type is a genetic disease[1].

Key Facts

  • spondylometaphyseal dysplasia, Kozlowski type's instance of is recorded as genetic disease[2].
  • spondylometaphyseal dysplasia, Kozlowski type's instance of is recorded as hereditary disorder[3].
  • spondylometaphyseal dysplasia, Kozlowski type's instance of is recorded as developmental defect during embryogenesis[4].
  • spondylometaphyseal dysplasia, Kozlowski type's instance of is recorded as rare disease[5].
  • spondylometaphyseal dysplasia, Kozlowski type's instance of is recorded as class of disease[6].
  • spondylometaphyseal dysplasia, Kozlowski type is a type of spondylometaphyseal dysplasia[7].
  • spondylometaphyseal dysplasia, Kozlowski type is a type of TRPV4-related bone disorder[8].
  • spondylometaphyseal dysplasia, Kozlowski type is a type of autosomal dominant disease[9].
  • spondylometaphyseal dysplasia, Kozlowski type is a type of metaphyseal dysplasia[10].
  • spondylometaphyseal dysplasia, Kozlowski type's genetic association is recorded as TRPV4[11].
  • spondylometaphyseal dysplasia, Kozlowski type's exact match is recorded as http://www.orpha.net/ORDO/Orphanet_93314[12].
  • spondylometaphyseal dysplasia, Kozlowski type's exact match is recorded as http://purl.obolibrary.org/obo/DOID_0111554[13].
  • spondylometaphyseal dysplasia, Kozlowski type's exact match is recorded as http://identifiers.org/doid/DOID:0111554[14].

References

Programmatic citations — every numbered marker resolves to a verifiable graph row below.

Direct Wikidata claims

  1. [2] . wikidata.org.
  2. [3] . wikidata.org.
  3. [4] . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  4. [5] . wikidata.org.
  5. [6] . wikidata.org.
  6. [7] . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  7. [8] . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  8. [9] . Disease Ontology. Retrieved . wikidata.org.
  9. [10] . Disease Ontology. Retrieved . wikidata.org.
  10. [11] . Q905695. Retrieved . search.clinicalgenome.org. Provenance: wikidata.org.
  11. [12] . wikidata.org.
  12. [13] . Disease Ontology. Retrieved . wikidata.org.
  13. [14] . Identifiers.org. registry.identifiers.org. Provenance: wikidata.org.

Class ancestry

  1. [1] . Wikidata. wikidata.org.

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APA 4ort.xyz Knowledge Graph. (2026). spondylometaphyseal dysplasia, Kozlowski type. Retrieved May 3, 2026, from https://4ort.xyz/entity/spondylometaphyseal-dysplasia-kozlowski-type
MLA “spondylometaphyseal dysplasia, Kozlowski type.” 4ort.xyz Knowledge Graph, 4ort.xyz, 3 May. 2026, https://4ort.xyz/entity/spondylometaphyseal-dysplasia-kozlowski-type.
BibTeX @misc{4ortxyz_spondylometaphyseal-dysplasia-kozlowski-type_2026, author = {{4ort.xyz Knowledge Graph}}, title = {{spondylometaphyseal dysplasia, Kozlowski type}}, year = {2026}, url = {https://4ort.xyz/entity/spondylometaphyseal-dysplasia-kozlowski-type}, note = {Accessed: 2026-05-03}}
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Edit History

Rolling log of changes to this entity's Wikidata record. Values shown reflect the current state of each edited property — follow the history link to see the precise diff for any edit.

  1. 5d ago · JhealdBatch bot · 2026-07-03 view diff on Wikidata ↗
    Mondo id MONDO_0008477
    Genetic association TRPV4
    Gard rare disease id 3047
    Orphanet id 93314
    + 13 other properties edited (see Wikidata diff for full list)
    "/* wbeditentity-update:0| */ QuickStatements 3.0 [[:toollabs:qs-dev/batch/39742|batch #39742]]: subclass of disease, not instance"
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