pulmonary alveolar proteinosis
lung disease that is characterized by abnormal accumulation of surfactant occurs within the alveoli, interfering with gas exchange
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Summary
pulmonary alveolar proteinosis is a designated intractable/rare disease[1]. It draws 603 Wikipedia views per month (designated intractable rare disease category, ranking #146 of 201).[2]
Key Facts
- Instance of: rare disease[3], class of disease[4]
- Subclass of: lung disease[5], alveolar lung disease[6], primary interstitial lung disease specific to childhood due to pulmonary surfactant protein anomalies[7]
- Commons category: Pulmonary alveolar proteinosis[8]
- Prevalence: 0.000005[9]
- External data available at URL: http://www.nanbyou.or.jp/entry/4774[10]
- ICD-9-CM: 516.0[11]
- NCI Thesaurus ID: C85037[12]
- Health specialty: pulmonology[13]
- Genetic association: CSF2RB[14], CSF2RA[15], ABCA3[16], SFTPC[17], SFTPB[18], HLA-DRB1[19]
- Age of onset: juvenile onset[20], adult onset[21], childhood onset[22]
- Exact match: http://purl.obolibrary.org/obo/DOID_12120[23], http://identifiers.org/doid/DOID:12120[24], http://purl.obolibrary.org/obo/HP_0006517[25], http://www.orpha.net/ORDO/Orphanet_264675[26]
- On focus list of Wikimedia project: WikiProject Medicine[27]
- Has phenotype: hypoxia[28], pulmonary alveolar proteinosis[29], cyanosis[30], dyspnea[31], macrophage-derived foam cell[32], cough[33], Crazy paving[34], pulmonary adventitious sound[35], clubbing[36], weight loss[37], fever[38], hemoptysis[39], fatigue[40], chest pain[41]
- P14541: 1DEPJY[42]
- P14914: D00747[43]
Why It Matters
pulmonary alveolar proteinosis has Wikipedia articles in 12 language editions, a strong signal of global cultural recognition.[44] It is known by 19 alternative names across languages and contexts.[45]