pulmonary alveolar proteinosis

lung disease that is characterized by abnormal accumulation of surfactant occurs within the alveoli, interfering with gas exchange
MedicalCondition designated_intractable_rare_disease Q448698
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pulmonary alveolar proteinosis

Summary

pulmonary alveolar proteinosis is a designated intractable/rare disease[1]. It draws 119 Wikipedia views per month (designated_intractable_rare_disease category, ranking #146 of 201).[2]

Key Facts

  • pulmonary alveolar proteinosis's instance of is recorded as designated intractable/rare disease[3].
  • pulmonary alveolar proteinosis's instance of is recorded as rare disease[4].
  • pulmonary alveolar proteinosis's instance of is recorded as class of disease[5].
  • pulmonary alveolar proteinosis is a type of lung disease[6].
  • pulmonary alveolar proteinosis is a type of alveolar lung disease[7].
  • pulmonary alveolar proteinosis is a type of primary interstitial lung disease specific to childhood due to pulmonary surfactant protein anomalies[8].
  • pulmonary alveolar proteinosis is a type of disease[9].
  • pulmonary alveolar proteinosis's Commons category is recorded as Pulmonary alveolar proteinosis[10].
  • pulmonary alveolar proteinosis's external data available at URL is recorded as http://www.nanbyou.or.jp/entry/4774[11].
  • pulmonary alveolar proteinosis's ICD-9-CM is recorded as 516.0[12].
  • pulmonary alveolar proteinosis's NCI Thesaurus ID is recorded as C85037[13].
  • pulmonary alveolar proteinosis's health specialty is recorded as pulmonology[14].
  • pulmonary alveolar proteinosis's genetic association is recorded as CSF2RB[15].
  • pulmonary alveolar proteinosis's genetic association is recorded as CSF2RA[16].
  • pulmonary alveolar proteinosis's genetic association is recorded as ABCA3[17].
  • pulmonary alveolar proteinosis's genetic association is recorded as SFTPC[18].
  • pulmonary alveolar proteinosis's genetic association is recorded as SFTPB[19].
  • pulmonary alveolar proteinosis's exact match is recorded as http://purl.obolibrary.org/obo/DOID_12120[20].
  • pulmonary alveolar proteinosis's exact match is recorded as http://identifiers.org/doid/DOID:12120[21].
  • pulmonary alveolar proteinosis's exact match is recorded as http://purl.obolibrary.org/obo/HP_0006517[22].
  • pulmonary alveolar proteinosis's exact match is recorded as http://www.orpha.net/ORDO/Orphanet_264675[23].
  • pulmonary alveolar proteinosis's on focus list of Wikimedia project is recorded as WikiProject Medicine[24].

Why It Matters

pulmonary alveolar proteinosis draws 119 Wikipedia views per month (designated_intractable_rare_disease category, ranking #146 of 201).[2] It has Wikipedia articles in 12 language editions, a strong signal of global cultural recognition.[25] It is known by 7 alternative names across languages and contexts.[26]

References

Programmatic citations — every numbered marker resolves to a verifiable graph row below.

Direct Wikidata claims

  1. [3] . ddrare.nibiohn.go.jp. Retrieved . ddrare.nibiohn.go.jp. Provenance: wikidata.org.
  2. [4] . wikidata.org.
  3. [5] . wikidata.org.
  4. [6] . Disease Ontology. Retrieved . wikidata.org.
  5. [7] . wikidata.org.
  6. [8] . wikidata.org.
  7. [9] . wikidata.org.
  8. [10] . wikidata.org.
  9. [11] . ddrare.nibiohn.go.jp. Retrieved . ddrare.nibiohn.go.jp. Provenance: wikidata.org.
  10. [12] . Disease Ontology. Retrieved . wikidata.org.
  11. [13] . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  12. [14] . wikidata.org.
  13. [15] . Adult-onset hereditary pulmonary alveolar proteinosis caused by a single-base deletion in CSF2RB. wikidata.org.
  14. [16] . Pulmonary alveolar proteinosis caused by deletion of the GM-CSFRalpha gene in the X chromosome pseudoautosomal region 1.. wikidata.org.
  15. [17] . ABCA3 gene mutations in newborns with fatal surfactant deficiency. wikidata.org.
  16. [18] . A mutation in the surfactant protein C gene associated with familial interstitial lung disease. wikidata.org.
  17. [19] . A mutation in the surfactant protein B gene responsible for fatal neonatal respiratory disease in multiple kindreds. wikidata.org.
  18. [20] . Disease Ontology. Retrieved . wikidata.org.
  19. [21] . Identifiers.org. registry.identifiers.org. Provenance: wikidata.org.
  20. [22] . Human Phenotype Ontology release 2018-03-08. Retrieved . wikidata.org.
  21. [23] . wikidata.org.
  22. [24] . wikidata.org.

Class ancestry

  1. [1] . Wikidata. wikidata.org.

Aggregate / graph-position facts

  1. [2] . Wikimedia Foundation. dumps.wikimedia.org.
  2. [25] . Wikidata sitelinks. wikidata.org.
  3. [26] . Wikidata aliases. wikidata.org.

📑 Cite this page

Use these citations when quoting this entity in research, articles, AI prompts, or wherever provenance matters. We aggregate Wikidata + Wikipedia + authoritative open-data sources; the stitched, scored, cross-referenced view is what 4ort.xyz contributes.

APA 4ort.xyz Knowledge Graph. (2026). pulmonary alveolar proteinosis. Retrieved May 3, 2026, from https://4ort.xyz/entity/pulmonary-alveolar-proteinosis
MLA “pulmonary alveolar proteinosis.” 4ort.xyz Knowledge Graph, 4ort.xyz, 3 May. 2026, https://4ort.xyz/entity/pulmonary-alveolar-proteinosis.
BibTeX @misc{4ortxyz_pulmonary-alveolar-proteinosis_2026, author = {{4ort.xyz Knowledge Graph}}, title = {{pulmonary alveolar proteinosis}}, year = {2026}, url = {https://4ort.xyz/entity/pulmonary-alveolar-proteinosis}, note = {Accessed: 2026-05-03}}
LLM prompt According to 4ort.xyz Knowledge Graph (aggregator of Wikidata, Wikipedia, and authoritative open-data sources): pulmonary alveolar proteinosis — https://4ort.xyz/entity/pulmonary-alveolar-proteinosis (retrieved 2026-05-03)

Canonical URL: https://4ort.xyz/entity/pulmonary-alveolar-proteinosis · Last refreshed:

Edit History

Rolling log of changes to this entity's Wikidata record. Values shown reflect the current state of each edited property — follow the history link to see the precise diff for any edit.

  1. 15d ago · Mowsenter · 2026-06-15 view diff on Wikidata ↗
    Subclass of
    On focus list of wikimedia project WikiProject Medicine
    Genetic association CSF2RB, CSF2RA, ABCA3 +2
    Subclass of lung disease, alveolar lung disease, primary interstitial lung disease specific to childhood due to pulmonary surfactant protein anomalies +1
    + 4 other properties edited (see Wikidata diff for full list)
    "/* wbsetreference-add:2| */ [[Property:P672]]: C08.381.719"
Live feed via Wikidata EventStreams. New edits appear within minutes of being made on Wikidata.