Leber congenital amaurosis 5

Leber congenital amaurosis that is characterized by severe visual dysfunction, nystagmus, the oculodigital sign, and a normal fundus with onset in infancy and has material basis in mutation in the LCA5 gene on chromosome 6q14.1
MedicalCondition rare_disease Q27677679
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Leber congenital amaurosis 5

Summary

Leber congenital amaurosis 5 is a rare disease[1].

Key Facts

  • Leber congenital amaurosis 5's instance of is recorded as rare disease[2].
  • Leber congenital amaurosis 5's instance of is recorded as class of disease[3].
  • Leber congenital amaurosis 5's subclass of is recorded as Leber congenital amaurosis[4].
  • Leber congenital amaurosis 5's subclass of is recorded as genetic disease[5].
  • Leber congenital amaurosis 5's subclass of is recorded as autosomal recessive disease[6].
  • Leber congenital amaurosis 5's MeSH descriptor ID is recorded as C536602[7].
  • Leber congenital amaurosis 5's OMIM ID is recorded as 604537[8].
  • Leber congenital amaurosis 5's Disease Ontology ID is recorded as DOID:0110215[9].
  • Leber congenital amaurosis 5's genetic association is recorded as LCA5[10].
  • Leber congenital amaurosis 5's exact match is recorded as http://purl.obolibrary.org/obo/DOID_0110215[11].
  • Leber congenital amaurosis 5's exact match is recorded as http://identifiers.org/doid/DOID:0110215[12].
  • Leber congenital amaurosis 5's UMLS CUI is recorded as C1858301[13].
  • Leber congenital amaurosis 5's ICD-10-CM is recorded as H35.5[14].
  • Leber congenital amaurosis 5's GARD rare disease ID is recorded as 9983[15].
  • Leber congenital amaurosis 5's on focus list of Wikimedia project is recorded as WikiProject Medicine[16].
  • Leber congenital amaurosis 5's Mondo ID is recorded as MONDO_0011473[17].
  • Leber congenital amaurosis 5's UniProt disease ID is recorded as DI-00633[18].

References

Programmatic citations — every numbered marker resolves to a verifiable graph row below.

Direct Wikidata claims

  1. [2] . wikidata.org.
  2. [3] . wikidata.org.
  3. [4] . Disease Ontology. Retrieved . wikidata.org.
  4. [5] . Disease Ontology. Retrieved . wikidata.org.
  5. [6] . Disease Ontology. Retrieved . wikidata.org.
  6. [7] . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  7. [8] . Disease Ontology. Retrieved . wikidata.org.
  8. [9] . Disease Ontology. Retrieved . wikidata.org.
  9. [10] . Q905695. Retrieved . wikidata.org.
  10. [11] . Disease Ontology. Retrieved . wikidata.org.
  11. [12] . Identifiers.org. registry.identifiers.org. Provenance: wikidata.org.
  12. [13] . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  13. [14] . Disease Ontology. Retrieved . wikidata.org.
  14. [15] . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  15. [16] . wikidata.org.
  16. [17] . wikidata.org.
  17. [18] . wikidata.org.

Class ancestry

  1. [1] . Wikidata. wikidata.org.

📑 Cite this page

Use these citations when quoting this entity in research, articles, AI prompts, or wherever provenance matters. We aggregate Wikidata + Wikipedia + authoritative open-data sources; the stitched, scored, cross-referenced view is what 4ort.xyz contributes.

APA 4ort.xyz Knowledge Graph. (2026). Leber congenital amaurosis 5. Retrieved May 3, 2026, from https://4ort.xyz/entity/leber-congenital-amaurosis-5
MLA “Leber congenital amaurosis 5.” 4ort.xyz Knowledge Graph, 4ort.xyz, 3 May. 2026, https://4ort.xyz/entity/leber-congenital-amaurosis-5.
BibTeX @misc{4ortxyz_leber-congenital-amaurosis-5_2026, author = {{4ort.xyz Knowledge Graph}}, title = {{Leber congenital amaurosis 5}}, year = {2026}, url = {https://4ort.xyz/entity/leber-congenital-amaurosis-5}, note = {Accessed: 2026-05-03}}
LLM prompt According to 4ort.xyz Knowledge Graph (aggregator of Wikidata, Wikipedia, and authoritative open-data sources): Leber congenital amaurosis 5 — https://4ort.xyz/entity/leber-congenital-amaurosis-5 (retrieved 2026-05-03)

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