lamin A/C congenital muscular dystrophy

congenital muscular dystrophy characterized by autosomal dominant inheritance that has material basis in heterozygous mutation in the LMNA gene on chromosome 1q22
MedicalCondition rare_disease Q27835675
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lamin A/C congenital muscular dystrophy

Summary

lamin A/C congenital muscular dystrophy is a rare disease[1]. It draws 1 Wikipedia views per month (rare_disease category, ranking #237 of 627).[2]

Key Facts

  • lamin A/C congenital muscular dystrophy's instance of is recorded as rare disease[3].
  • lamin A/C congenital muscular dystrophy's instance of is recorded as class of disease[4].
  • lamin A/C congenital muscular dystrophy's subclass of is recorded as congenital muscular dystrophy[5].
  • lamin A/C congenital muscular dystrophy's subclass of is recorded as genetic disease[6].
  • lamin A/C congenital muscular dystrophy's subclass of is recorded as autosomal dominant disease[7].
  • lamin A/C congenital muscular dystrophy's MeSH descriptor ID is recorded as C567708[8].
  • lamin A/C congenital muscular dystrophy's OMIM ID is recorded as 613205[9].
  • lamin A/C congenital muscular dystrophy's Disease Ontology ID is recorded as DOID:0110640[10].
  • lamin A/C congenital muscular dystrophy's Orphanet ID is recorded as 157973[11].
  • lamin A/C congenital muscular dystrophy's health specialty is recorded as neurology[12].
  • lamin A/C congenital muscular dystrophy's genetic association is recorded as LMNA[13].
  • lamin A/C congenital muscular dystrophy's exact match is recorded as http://purl.obolibrary.org/obo/DOID_0110640[14].
  • lamin A/C congenital muscular dystrophy's exact match is recorded as http://identifiers.org/doid/DOID:0110640[15].
  • lamin A/C congenital muscular dystrophy's UMLS CUI is recorded as C2750785[16].
  • lamin A/C congenital muscular dystrophy's ICD-10-CM is recorded as G71.2[17].
  • lamin A/C congenital muscular dystrophy's GARD rare disease ID is recorded as 12585[18].
  • lamin A/C congenital muscular dystrophy's on focus list of Wikimedia project is recorded as WikiProject Medicine[19].
  • lamin A/C congenital muscular dystrophy's Mondo ID is recorded as MONDO_0013178[20].
  • lamin A/C congenital muscular dystrophy's Genetics Home Reference Conditions ID is recorded as lmna-related-congenital-muscular-dystrophy[21].
  • lamin A/C congenital muscular dystrophy's UniProt disease ID is recorded as DI-02702[22].

Why It Matters

lamin A/C congenital muscular dystrophy draws 1 Wikipedia views per month (rare_disease category, ranking #237 of 627).[2]

References

Programmatic citations — every numbered marker resolves to a verifiable graph row below.

Direct Wikidata claims

  1. [3] . wikidata.org.
  2. [4] . wikidata.org.
  3. [5] . Disease Ontology. Retrieved . wikidata.org.
  4. [6] . Disease Ontology. Retrieved . wikidata.org.
  5. [7] . Disease Ontology. Retrieved . wikidata.org.
  6. [8] . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  7. [9] . Disease Ontology. Retrieved . wikidata.org.
  8. [10] . Disease Ontology. Retrieved . wikidata.org.
  9. [11] . Disease Ontology. Retrieved . wikidata.org.
  10. [12] . wikidata.org.
  11. [13] . Q905695. Retrieved . platform.opentargets.org. Provenance: wikidata.org.
  12. [14] . Disease Ontology. Retrieved . wikidata.org.
  13. [15] . Identifiers.org. registry.identifiers.org. Provenance: wikidata.org.
  14. [16] . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  15. [17] . Disease Ontology. Retrieved . wikidata.org.
  16. [18] . Monarch Disease Ontology release 2018-06-29. Retrieved . wikidata.org.
  17. [19] . wikidata.org.
  18. [20] . wikidata.org.
  19. [21] . wikidata.org.
  20. [22] . wikidata.org.

Class ancestry

  1. [1] . Wikidata. wikidata.org.

Aggregate / graph-position facts

  1. [2] . Wikimedia Foundation. dumps.wikimedia.org.

📑 Cite this page

Use these citations when quoting this entity in research, articles, AI prompts, or wherever provenance matters. We aggregate Wikidata + Wikipedia + authoritative open-data sources; the stitched, scored, cross-referenced view is what 4ort.xyz contributes.

APA 4ort.xyz Knowledge Graph. (2026). lamin A/C congenital muscular dystrophy. Retrieved May 3, 2026, from https://4ort.xyz/entity/lamin-a-c-congenital-muscular-dystrophy
MLA “lamin A/C congenital muscular dystrophy.” 4ort.xyz Knowledge Graph, 4ort.xyz, 3 May. 2026, https://4ort.xyz/entity/lamin-a-c-congenital-muscular-dystrophy.
BibTeX @misc{4ortxyz_lamin-a-c-congenital-muscular-dystrophy_2026, author = {{4ort.xyz Knowledge Graph}}, title = {{lamin A/C congenital muscular dystrophy}}, year = {2026}, url = {https://4ort.xyz/entity/lamin-a-c-congenital-muscular-dystrophy}, note = {Accessed: 2026-05-03}}
LLM prompt According to 4ort.xyz Knowledge Graph (aggregator of Wikidata, Wikipedia, and authoritative open-data sources): lamin A/C congenital muscular dystrophy — https://4ort.xyz/entity/lamin-a-c-congenital-muscular-dystrophy (retrieved 2026-05-03)

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