# fibronectin glomerulopathy

> Fibronectin glomerulopathy is a hereditary kidney disease characterized by proteinuria, type IV renal tubular acidosis, microscopic hematuria and hypertension that may lead to end-stage renal failure in the second to sixth decade of life

**Wikidata**: [Q55780814](https://www.wikidata.org/wiki/Q55780814)  
**Source**: https://4ort.xyz/entity/fibronectin-glomerulopathy


## References

1. Monarch Disease Ontology release 2018-06-29
2. Mutations in FN1 cause glomerulopathy with fibronectin deposits.